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Mon Apr 4 11:09:44 2005
Papers with one of the following phrases in the title:
fragile x or FMRP or trinucleotitde expansion or nucleotide expansion or cgg

Nodes: 2647, Authors: 5321, Journals: 428, Outer References: 16458, Words: 3536
Collection span: 1967 - 2005
View: Overview. Sorted by journal name.
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#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
1011579 1997 A N A E-APPROCHE NEUROPSYCHOLOGIQUE DES APPRENTISSAGES CHEZ L ENFANT 9(5):191-192
Fombonne E
The fragile X syndrome
00
214251580 1997 A N A E-APPROCHE NEUROPSYCHOLOGIQUE DES APPRENTISSAGES CHEZ L ENFANT 9(5):195-201
Mandel JL
The fragile X mental retardation syndrome: the FMR1 gene and its mutations
00
313241581 1997 A N A E-APPROCHE NEUROPSYCHOLOGIQUE DES APPRENTISSAGES CHEZ L ENFANT 9(5):202-208
Hagerman RJ
Fragile X syndrome: meeting the challenges of diagnosis and care
00
412161582 1997 A N A E-APPROCHE NEUROPSYCHOLOGIQUE DES APPRENTISSAGES CHEZ L ENFANT 9(5):209-212
Fombonne E
Epidemiological studies of fragile X syndrome
00
5891583 1997 A N A E-APPROCHE NEUROPSYCHOLOGIQUE DES APPRENTISSAGES CHEZ L ENFANT 9(5):221-223
Ponsot G
Fragile X syndrome. Early recognition.
00
6691584 1997 A N A E-APPROCHE NEUROPSYCHOLOGIQUE DES APPRENTISSAGES CHEZ L ENFANT 9(5):224-226
Gerard CL; Guillotte E; Servel F; Barbeau M
Assessment and remediation of communication disorders in children with fragile X syndrome
00
73101585 1997 A N A E-APPROCHE NEUROPSYCHOLOGIQUE DES APPRENTISSAGES CHEZ L ENFANT 9(5):227-231
Roge B
Fragile X syndrome. Special education: the French context
00
813271586 1997 A N A E-APPROCHE NEUROPSYCHOLOGIQUE DES APPRENTISSAGES CHEZ L ENFANT 9(5):232-238
Turk J
Treatments and services for individuals with fragile X syndrome and their families
00
9002093 2001 ABSTRACTS OF PAPERS OF THE AMERICAN CHEMICAL SOCIETY 221:U3-U3
Rodesittisuk P; Romero RM; Haworth IS
Conformation of fragile X-associated triplet repeat DNA containing C-C mismatch pairs.
00
1015191440 1996 ACTA BIOCHIMICA POLONICA 43(2):383-388
Milewski M; Zygulska M; Bal J; Deelen WH; Obersztyn E; et al.
Analysis of unstable DNA sequence in FRM1 gene in Polish families with fragile X syndrome
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
1100315 1986 ACTA NEUROLOGICA SCANDINAVICA 73(4):447-448
BAKKE JV
FRAGILE-X SYNDROME AS A CONCOMITANT TO AND PROBABLE CAUSE OF MENTAL-RETARDATION
00
12752238 1985 ACTA NEUROPATHOLOGICA 67(3-4):289-295
RUDELLI RD; BROWN WT; WISNIEWSKI K; JENKINS EC; LAUREKAMIONOWSKA M; et al.
ADULT FRAGILE X-SYNDROME - CLINICO-NEUROPATHOLOGIC FINDINGS
77116
1316282216 2002 ACTA PAEDIATRICA 91(5):535-539
Hecimovic S; Tarnik IP; Baric I; Cakarun Z; Pavelic K
Screening for fragile X syndrome: results from a school for mentally retarded children
11
1437239 1985 ACTA PAEDIATRICA SCANDINAVICA 74(6):974-974
FLOOD A; SANNER G
REFRACTIVE ERRORS IN THE FRAGILE-X SYNDROME
33
155102479 2004 ACTA PHARMACOLOGICA SINICA 25(7):973-976
Sun YJ; Han X
Dynamic behavior of fragile X full mutations in cultured female fetal fibroblasts
00
16519166 1984 ACTA PSYCHIATRICA SCANDINAVICA 70(5):510-514
JORGENSEN OS; NIELSEN KB; ISAGER T; MOURIDSEN SE
FRAGILE X-CHROMOSOME AMONG CHILD PSYCHIATRIC-PATIENTS WITH DISTURBANCES OF LANGUAGE AND SOCIAL RELATIONSHIPS - A PILOT-STUDY
1221
171552167 1984 ALABAMA JOURNAL OF MEDICAL SCIENCES 21(1):68-72
SCARBROUGH PR; COSPER P; FINLEY SC; SMITH NB
FRAGILE-X SYNDROME - AN OVERVIEW
03
18515168 1984 ALABAMA JOURNAL OF MEDICAL SCIENCES 21(3):284-286
MIXON JC; DEV VG
UNDERSTANDING THE FRAGILE X-SYNDROME
02
1900169 1984 ALABAMA JOURNAL OF MEDICAL SCIENCES 21(3):322-322
MIXON JC
INHIBITION OF FRAGILE-X EXPRESSION BY 5-AZACYTIDINE (AZA) AND BY S-ADENOSYLHOMOCYSTEINE (SAH)
00
2000615 1989 AMERICAN FAMILY PHYSICIAN 39(5):185-193
SIMENSEN RJ; ROGERS RC
FRAGILE-X SYNDROME
11
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
21001030 1993 AMERICAN FAMILY PHYSICIAN 47(5):1072-1073
SIMENSEN RJ
FRAGILE-X SYNDROME
00
22126240 1985 AMERICAN JOURNAL OF DANCE THERAPY 8:67-80
WOLFSCHEIN EG; FISCH GS; COHEN IL
A STUDY OF THE USE OF NONVERBAL SYSTEMS IN THE DIFFERENTIAL-DIAGNOSIS OF AUTISTIC, MENTALLY-RETARDED AND FRAGILE X-INDIVIDUALS
00
2313038 1982 AMERICAN JOURNAL OF DISEASES OF CHILDREN 136(5):389-391
TOWNES PL
FRAGILE-X SYNDROME - A JIGSAW PUZZLE WITH PICTURE EMERGING
68
2423539 1982 AMERICAN JOURNAL OF DISEASES OF CHILDREN 136(5):392-398
CARPENTER NJ; LEICHTMAN LG; SAY B
FRAGILE X-LINKED MENTAL-RETARDATION - A SURVEY OF 65 PATIENTS WITH MENTAL-RETARDATION OF UNKNOWN ORIGIN
4965
25924241 1985 AMERICAN JOURNAL OF DISEASES OF CHILDREN 139(7):674-678
HAGERMAN R; KEMPER M; HUDSON M
LEARNING-DISABILITIES AND ATTENTIONAL PROBLEMS IN BOYS WITH THE FRAGILE X-SYNDROME
5572
2614316 1986 AMERICAN JOURNAL OF DISEASES OF CHILDREN 140(4):327-327
BOWERS EJ
FRAGILE-X SYNDROME AND LEARNING-DISABILITIES
12
2717317 1986 AMERICAN JOURNAL OF DISEASES OF CHILDREN 140(4):327-328
HAGERMAN RJ
FRAGILE-X SYNDROME AND LEARNING-DISABILITIES - REPLY
11
28536415 1987 AMERICAN JOURNAL OF DISEASES OF CHILDREN 141(2):184-187
HAGERMAN RJ; ALTSHULSTARK D; MCBOGG P
RECURRENT OTITIS-MEDIA IN THE FRAGILE X-SYNDROME
914
2914416 1987 AMERICAN JOURNAL OF DISEASES OF CHILDREN 141(6):601-601
BARTOLUCCI G; SZATMARI P
POSSIBLE SIMILARITIES BETWEEN THE FRAGILE-X AND ASPERGERS SYNDROMES
12
3011417 1987 AMERICAN JOURNAL OF DISEASES OF CHILDREN 141(6):601-602
HAGERMAN RJ
POSSIBLE SIMILARITIES BETWEEN THE FRAGILE-X AND ASPERGERS SYNDROMES - REPLY
11
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
311744499 1988 AMERICAN JOURNAL OF DISEASES OF CHILDREN 142(11):1216-1221
HAGERMAN R; BERRY R; JACKSON AW; CAMPBELL J; SMITH ACM; et al.
INSTITUTIONAL SCREENING FOR THE FRAGILE-X SYNDROME
1322
328141031 1993 AMERICAN JOURNAL OF DISEASES OF CHILDREN 147(6):605-606
GOLDSON E; HAGERMAN RJ
FRAGILE-X SYNDROME AND FAILURE-TO-THRIVE
44
3320271032 1993 AMERICAN JOURNAL OF DISEASES OF CHILDREN 147(7):723-726
STALEY LW; HULL CE; MAZZOCCO MMM; THIBODEAU SN; SNOW K; et al.
MOLECULAR-CLINICAL CORRELATIONS IN CHILDREN AND ADULTS WITH FRAGILE X-SYNDROME
2124
3423291033 1993 AMERICAN JOURNAL OF DISEASES OF CHILDREN 147(11):1231-1235
RAMOS FJ; EUNPU DL; FINUCANE B; PFENDNER EG
DIRECT DNA TESTING FOR FRAGILE-X SYNDROME
12
3529361034 1993 AMERICAN JOURNAL OF DISEASES OF CHILDREN 147(11):1236-1241
HULL C; HAGERMAN RJ
A STUDY OF THE PHYSICAL, BEHAVIORAL, AND MEDICAL PHENOTYPE, INCLUDING ANTHROPOMETRIC MEASURES, OF FEMALES WITH FRAGILE-X SYNDROME
2939
36001284 1995 AMERICAN JOURNAL OF EPIDEMIOLOGY 141(11):S50-S50
DAWSON DV; LACHIEWICZ AM
BEHAVIORAL EPIDEMIOLOGY OF FRAGILE-X SYNDROME IN FEMALE PEDIATRIC POPULATIONS
00
37014 1980 AMERICAN JOURNAL OF HUMAN GENETICS 32(6):A73-A73
JACKY PB
EXPRESSION IN FIBROBLAST-CULTURE OF THE FRAGILE X-CHROMOSOME ASSOCIATED WITH FAMILIAL SEX-LINKED MENTAL-RETARDATION - FACTORS INFLUENCING A RELIABLE DETERMINATION OF THE FREQUENCY OF EXPRESSION
00
38005 1980 AMERICAN JOURNAL OF HUMAN GENETICS 32(6):A114-A114
KAISERMCCAW B; HECHT F
THE FRAGILE-X - NO DYSMORPHIC SYNDROME, BUT A MARKER
22
390248 1981 AMERICAN JOURNAL OF HUMAN GENETICS 33(5):752-761
MARENI C; MIGEON BR
FRAGILE-X SYNDROME - SEARCH FOR PHENOTYPIC MANIFESTATIONS AT LOCI FOR HYPOXANTHINE PHOSPHORIBOSYLTRANSFERASE AND GLUCOSE-6-PHOSPHATE-DEHYDROGENASE
710
40009 1981 AMERICAN JOURNAL OF HUMAN GENETICS 33(6):A99-A99
BRYANT EM; HOEHN H; MARTIN GM
EXPRESSION OF THE FRAGILE X IN EUPLOID SOMATIC-CELL HYBRIDS
33
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
410010 1981 AMERICAN JOURNAL OF HUMAN GENETICS 33(6):A100-A100
CARPENTER NJ; LEICHTMAN LG; LOGAN A; SAY B
FRAGILE X-LINKED MENTAL-RETARDATION
11
420011 1981 AMERICAN JOURNAL OF HUMAN GENETICS 33(6):A107-A107
HOWARDPEEBLES PN; FINLEY WH
TESTICULAR AND CYTOGENETIC SCREENING OF RETARDED MALES FROM THE SOUTH FOR THE FRAGILE X-LINKED MENTAL-RETARDATION SYNDROME
11
430012 1981 AMERICAN JOURNAL OF HUMAN GENETICS 33(6):A122-A122
SHAPIRO LR; KUHR MD; WILMOT PL; LILIENTHAL ER; HIGGS LC
MULTIPLE SIBLING MENTAL-RETARDATION AND THE IMPACT OF THE FRAGILE X-CHROMOSOME
11
4401840 1982 AMERICAN JOURNAL OF HUMAN GENETICS 34(2):286-293
UCHIDA IA; JOYCE EM
ACTIVITY OF THE FRAGILE-X IN HETEROZYGOUS CARRIERS
066
450041 1982 AMERICAN JOURNAL OF HUMAN GENETICS 34(6):A82-A82
BROWN T; JENKINS E; FRIEDMAN E; BROOKS J; DUNCAN C; et al.
A CONTROLLED TRIAL OF FOLIC-ACID THERAPY IN FRAGILE-X INDIVIDUALS
33
460042 1982 AMERICAN JOURNAL OF HUMAN GENETICS 34(6):A93-A93
HAVKIN S; CHAKI R; GOLDMAN B
FRAGILE X-CHROMOSOME IN 2 FAMILIES WITH X-LINKED MENTAL-RETARDATION
11
470043 1982 AMERICAN JOURNAL OF HUMAN GENETICS 34(6):A103-A103
NOLIN S; BROWN T; JENKINS E
FRAGILE-X SYNDROME - DILEMMAS FOR GENETIC-COUNSELING
11
480044 1982 AMERICAN JOURNAL OF HUMAN GENETICS 34(6):A110-A110
SHAPIRO LR; HASEN J; GORDON G; SOUTHREN AL; WILMOT PL; et al.
TESTICULAR INSUFFICIENCY AND DISORDERED THYROID METABOLISM IN THE FRAGILE X-CHROMOSOME SYNDROME
57
490045 1982 AMERICAN JOURNAL OF HUMAN GENETICS 34(6):A121-A121
CHUDLEY AE; KNOLL J; GERRARD JW; SHEPEL L; MCGAHEY E; et al.
FRAGILE X-LINKED MENTAL-RETARDATION - EFFECT OF AGE AND INTELLIGENCE ON EXPRESSION OF FRAGILE-X
11
500346 1982 AMERICAN JOURNAL OF HUMAN GENETICS 34(6):A129-A129
HOWARDPEEBLES PN
FRAGILE X-CHROMOSOME - THE ROLE OF METHIONINE AND OTHER INVITRO MANIPULATIONS
45
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
510347 1982 AMERICAN JOURNAL OF HUMAN GENETICS 34(6):A130-A130
JENKINS E; BROWN T; DUNCAN C; BROOKS J
FRAGILE X-CHROMOSOME PRENATAL-DIAGNOSIS
34
520048 1982 AMERICAN JOURNAL OF HUMAN GENETICS 34(6):A131-A131
KNOLL J; CHUDLEY AE; GERRARD JW
EFFICACY OF FUDR IN ENHANCING EXPRESSION OF FRA(X) IN AFFECTED MALES AND CARRIER FEMALES WITH FRAGILE X-LINKED MENTAL-RETARDATION
11
530149 1982 AMERICAN JOURNAL OF HUMAN GENETICS 34(6):A149-A149
WANG JC; BOSS GR; MAGNER MT; ERBE RW
FOLATE PATHWAYS IN CELLS FROM FRAGILE-X SYNDROME PATIENTS AND CARRIERS
23
5421389 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(5):861-868
UCHIDA IA; FREEMAN VCP; JAMRO H; PARTINGTON MW; SOLTAN HC
ADDITIONAL EVIDENCE FOR FRAGILE-X ACTIVITY IN HETEROZYGOUS CARRIERS
2533
5552690 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(5):869-878
POPOVICH BW; ROSENBLATT DS; COOPER BA; VEKEMANS M
INTRACELLULAR FOLATE DISTRIBUTION IN CULTURED FIBROBLASTS FROM PATIENTS WITH THE FRAGILE-X SYNDROME
812
560091 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A81-A81
BROWN T; JENKINS E; SHAPIRO LR
FRAGILE (X) SYNDROME PRENATAL-DIAGNOSIS REGISTRY
00
570192 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A82-A82
CARPENTER NJ; BARBER DH; JONES M; LINDLEY W; CARR C
CONTROLLED 6-MONTH STUDY OF ORAL FOLIC-ACID THERAPY IN BOYS WITH FRAGILE X-LINKED MENTAL-RETARDATION
09
580093 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A92-A92
HAGERMAN R; MCBOGG P; LEVITUS A; MCGAVRAN L; SMITH A; et al.
FOLIC-ACID TREATMENT OF THE FRAGILE-X SYNDROME
34
590094 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A117-A117
SHAPIRO LR; SUMMA GM; WILMOT PL; GLOTH E
SCREENING AND DETECTION OF THE FRAGILE X-SYNDROME
00
600195 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A122-A122
WILSON DP; CARPENTER NJ; BERKOVITZ GD; BROWN TR; MIGEON CJ
THYROID-FUNCTION IN FRAGILE X-LINKED MENTAL-RETARDATION
22
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
610096 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A127-A127
BRYANT EM; GLADSTONE P; MARTIN GM
EXPRESSION OF THE FRAGILE-X IN MOUSE-X HUMAN SOMATIC-CELL HYBRIDS
22
620097 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A131-A131
EREN M; DISTECHE C
BEHAVIORAL-PHENOTYPE OF THE FRAGILE X-SYNDROME - RELATIONSHIP BETWEEN FREQUENCY OF MARKER-X, MENTAL-RETARDATION AND VERBAL DISABILITY
35
630098 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A135-A135
HOWARDPEEBLES PN
FRAGILE X-CHROMOSOME - TECHNICAL ASPECTS FOR MAXIMIZING EXPRESSION
00
640099 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A136-A136
JENKINS E; DUNCAN C; BROOKS J; LELE K; SANZ M; et al.
LOW-FREQUENCY FRAGILE X-CHROMOSOMES IN CULTURES FROM NORMAL PEOPLE
04
6500100 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A139-A139
KNOLL JH; CHUDLEY AE; GERRARD JW
FREQUENCY AND REPLICATION PATTERN OF FRAGILE (X) (Q28) IN HETEROZYGOTES
00
6602101 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A144-A144
MIXON C; DEV VG
INHIBITION OF FRAGILE-X EXPRESSION BY 5-AZACYTIDINE (AZA) AND BY S-ADENOSYLHOMOCYSTEINE (SAH)
00
6700102 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A146-A146
OBRIEN MM; PADREMENDOZA T; PUESCHEL SM
MATERNAL NONDISJUNCTION OF FRAGILE X-CHROMOSOME RESULTING IN KLINEFELTER SYNDROME
12
6800103 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A159-A159
WANG JC; BEARDSLEY GP; ERBE RW
THYMIDYLATE METABOLISM AND URACIL MISINCORPORATION IN FRAGILE-X SYNDROME CELLS
02
6900104 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A161-A161
WILLEY A; HATCHER N; HEALY N
FRAGILE-X FAMILIES - GENETIC INSTABILITY, OR UNEXPECTED CYTOGENETIC ABERRATIONS
00
7000105 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A162-A162
WILSON MG; MARCHESE CA; LIN MS; HERBERT WS; PERDELWITZ M
PRENATAL-DIAGNOSIS OF FRAGILE-X IN A HETEROZYGOUS FEMALE FETUS AND POSTNATAL FOLLOW-UP
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
7100106 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):A174-A174
HOLDEN J; BECKETT J; MULLIGAN L; PHILLIPS A; SIMPSON N; et al.
A SEARCH FOR RESTRICTION FRAGMENT LENGTH POLYMORPHISMS (RFLPS) LINKED TO THE FRAGILE-X FORM OF X-LINKED MENTAL-RETARDATION
03
72213107 1983 AMERICAN JOURNAL OF HUMAN GENETICS 35(6):1270-1275
MIXON JC; DEV VG
FRAGILE-X EXPRESSION IS DECREASED BY 5-AZACYTIDINE AND S-ADENOSYLHOMOCYSTEINE
59
7304170 1984 AMERICAN JOURNAL OF HUMAN GENETICS 36(1):227-229
MIEZEJESKI CM; JENKINS EC; HILL AL; WISNIEWSKI K; BROWN WT
VERBAL VS NONVERBAL ABILITY, FRAGILE-X SYNDROME, AND HETEROZYGOUS CARRIERS
89
74419171 1984 AMERICAN JOURNAL OF HUMAN GENETICS 36(3):640-645
KNOLL JH; CHUDLEY AE; GERRARD JW
FRAGILE (X) X-LINKED MENTAL-RETARDATION .2. FREQUENCY AND REPLICATION PATTERN OF FRAGILE (X) (Q28) IN HETEROZYGOTES
2031
75617242 1985 AMERICAN JOURNAL OF HUMAN GENETICS 37(1):193-198
ABRUZZO MA; MAYER M; JACOBS PA
THE EFFECT OF METHIONINE AND 5-AZACYTIDINE ON FRAGILE-X EXPRESSION
35
76829243 1985 AMERICAN JOURNAL OF HUMAN GENETICS 37(3):463-472
MULLIGAN LM; PHILLIPS MA; FORSTERGIBSON CJ; BECKETT J; PARTINGTON MW; et al.
GENETIC-MAPPING OF DNA SEGMENTS RELATIVE TO THE LOCUS FOR THE FRAGILE-X SYNDROME AT XQ27.3
649
771129244 1985 AMERICAN JOURNAL OF HUMAN GENETICS 37(3):543-552
ROSENBLATT DS; DUSCHENES EA; HELLSTROM FV; GOLICK MS; VEKEMANS MJJ; et al.
FOLIC-ACID BLINDED TRIAL IN IDENTICAL-TWINS WITH FRAGILE-X SYNDROME
913
78418245 1985 AMERICAN JOURNAL OF HUMAN GENETICS 37(5):947-955
CANTU ES; NUSSBAUM RL; AIRHART SD; LEDBETTER DH
FRAGILE (X) EXPRESSION INDUCED BY FUDR IS TRANSIENT AND INVERSELY RELATED TO LEVELS OF THYMIDYLATE SYNTHASE ACTIVITY
35
79923246 1985 AMERICAN JOURNAL OF HUMAN GENETICS 37(5):956-964
HOWARDPEEBLES PN; FRIEDMAN JM
UNAFFECTED CARRIER MALES IN FAMILIES WITH FRAGILE-X SYNDROME
1419
80228247 1985 AMERICAN JOURNAL OF HUMAN GENETICS 37(6):1192-1205
NUSSBAUM RL; WALMSLEY RM; LESKO JG; AIRHART SD; LEDBETTER DH
THYMIDYLATE SYNTHASE-DEFICIENT CHINESE-HAMSTER CELLS - A SELECTION SYSTEM FOR HUMAN-CHROMOSOME 18 AND EXPERIMENTAL SYSTEM FOR THE STUDY OF THYMIDYLATE SYNTHASE REGULATION AND FRAGILE-X EXPRESSION
647
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
81524318 1986 AMERICAN JOURNAL OF HUMAN GENETICS 38(3):309-318
GLOVER TW; COYLEMORRIS J; PEARCEBIRGE L; BERGER C; GEMMILL RM
DNA DEMETHYLATION INDUCED BY 5-AZACYTIDINE DOES NOT AFFECT FRAGILE-X EXPRESSION
36
82417319 1986 AMERICAN JOURNAL OF HUMAN GENETICS 38(4):533-539
ABRUZZO MA; HUNT PA; MAYER M; JACOBS PA; WANG JCC; et al.
A COMPARISON OF FRAGILE X-EXPRESSION IN LYMPHOCYTE AND LYMPHOBLASTOID CULTURES
23
831230500 1988 AMERICAN JOURNAL OF HUMAN GENETICS 42(2):380-389
ARVEILER B; OBERLE I; VINCENT A; HOFKER MH; PEARSON PL; et al.
GENETIC-MAPPING OF THE XQ27-Q28 REGION - NEW RFLP MARKERS USEFUL FOR DIAGNOSTIC APPLICATIONS IN FRAGILE-X AND HEMOPHILIA-B FAMILIES
2261
841024501 1988 AMERICAN JOURNAL OF HUMAN GENETICS 43(1):46-51
ARINAMI T; SATO M; NAKAJIMA S; KONDO I
AUDITORY BRAIN-STEM RESPONSES IN THE FRAGILE-X SYNDROME
811
85831502 1988 AMERICAN JOURNAL OF HUMAN GENETICS 43(5):684-688
PATTERSON M; BELL M; KRESS W; DAVIES KE; FROSTERISKENIUS U
LINKAGE STUDIES IN A LARGE FRAGILE X-FAMILY
1023
861429616 1989 AMERICAN JOURNAL OF HUMAN GENETICS 45(2):304-309
DAHL N; GOONEWARDENA P; MALMGREN H; GUSTAVSON KH; HOLMGREN G; et al.
LINKAGE ANALYSIS OF FAMILIES WITH FRAGILE-X MENTAL-RETARDATION, USING A NOVEL RFLP MARKER (DXS 304)
1940
87924617 1989 AMERICAN JOURNAL OF HUMAN GENETICS 45(5):697-705
REISS AL; FREUND L; VINOGRADOV S; HAGERMAN R; CRONISTER A
PARENTAL INHERITANCE AND PSYCHOLOGICAL DISABILITY IN FRAGILE-X FEMALES
2631
88410618 1989 AMERICAN JOURNAL OF HUMAN GENETICS 45(6):977-978
FERRI R
BRAIN-STEM AUDITORY EVOKED-POTENTIALS IN THE FRAGILE-X SYNDROME
23
8927619 1989 AMERICAN JOURNAL OF HUMAN GENETICS 45(6):978-979
ARINAMI T
BRAIN-STEM AUDITORY EVOKED-POTENTIALS IN THE FRAGILE-X SYNDROME - REPLY
00
90514674 1990 AMERICAN JOURNAL OF HUMAN GENETICS 46(3):443-451
SVED JA; LAIRD CD
POPULATION GENETIC CONSEQUENCES OF THE FRAGILE-X SYNDROME, BASED ON THE X-INACTIVATION IMPRINTING MODEL
1222
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
911966675 1990 AMERICAN JOURNAL OF HUMAN GENETICS 46(4):696-719
LAIRD CD; LAMB MM; THORNE JL
2 PROGENITOR CELLS FOR HUMAN OOGONIA INFERRED FROM PEDIGREE DATA AND THE X-INACTIVATION IMPRINTING MODEL OF THE FRAGILE-X SYNDROME
2834
921233676 1990 AMERICAN JOURNAL OF HUMAN GENETICS 46(4):738-743
ROCCHI M; ARCHIDIACONO N; RINALDI A; FILIPPI G; BARTOLUCCI G; et al.
MENTAL-RETARDATION IN HETEROZYGOTES FOR THE FRAGILE-X MUTATION - EVIDENCE IN FAVOR OF AN X INACTIVATION-DEPENDENT EFFECT
1113
931144677 1990 AMERICAN JOURNAL OF HUMAN GENETICS 46(4):744-753
KHALIFA MM; REISS AL; MIGEON BR
METHYLATION STATUS OF GENES FLANKING THE FRAGILE SITE IN MALES WITH THE FRAGILE-X SYNDROME - A TEST OF THE IMPRINTING HYPOTHESIS
47
941837678 1990 AMERICAN JOURNAL OF HUMAN GENETICS 47(2):175-180
BROWN WT
INVITED EDITORIAL - THE FRAGILE-X - PROGRESS TOWARD SOLVING THE PUZZLE
2941
95624679 1990 AMERICAN JOURNAL OF HUMAN GENETICS 47(2):181-187
MACKINNON RN; HIRST MC; BELL MV; WATSON JEV; CLAUSSEN U; et al.
MICRODISSECTION OF THE FRAGILE-X REGION
937
96638680 1990 AMERICAN JOURNAL OF HUMAN GENETICS 47(2):187-195
SUTHERS GK; HYLAND VJ; CALLEN DF; OBERLE I; ROCCHI M; et al.
PHYSICAL MAPPING OF NEW DNA PROBES NEAR THE FRAGILE-X MUTATION (FRAXA) BY USING A PANEL OF CELL-LINES
2664
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FRAGILE-X TESTING OF FAMILY MEMBERS IN THE CLINICAL CYTOGENETICS LABORATORY - PERIMETERS AND PITFALLS
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LINKAGE TO DXS52 IN A FRAGILE-X NEGATIVE FAMILY
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CONSTRUCTION OF A 600-KB YAC CONTIG PROXIMAL TO THE FRAGILE X-SITE
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NEUROBEHAVIORAL EFFECTS OF THE FRAGILE-X PREMUTATION IN ADULT WOMEN - A CONTROLLED-STUDY
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MUTATIONAL PREVALENCE OF FRAGILE X-PREMUTATIONS IN 10,624 FEMALES FROM THE GENERAL-POPULATION BY SOUTHERN BLOTTING
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FRAGILE X-SYNDROME IS ASSOCIATED WITH A LARGE DOMAIN OF DELAYED REPLICATION AT THE FMR1 LOCUS
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THE PROTEIN PRODUCT OF THE FRAGILE X-GENE, FMR-1, HAS CHARACTERISTICS OF AN RNA-BINDING PROTEIN
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FRAGILE-X PRENATAL-DIAGNOSIS IN KNOWN CARRIERS
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THE FRAGILE X SYNDROME - A FAMILY WITH 3 HOMOZYGOUS FRA(X) SISTERS
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THE FRAGILE-X SYNDROME AND PREMATURE MENOPAUSE
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MONOZYGOTIC TWINS DISCORDANT FOR THE FRAGILE-X SYNDROME (FXS)
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ABNORMAL CHROMATIN STRUCTURE ASSOCIATED WITH THE FULL FRAGILE-X MUTATION
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STABILITY OF THE CGG REPEAT REGION OF FMR-1
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A 2ND HYPERMUTABLE DNA-SEQUENCE LOCATED WITHIN THE FRAGILE X-GENE
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FOUNDER FRAGILE-X CHROMOSOMES
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STRONG FOUNDER EFFECT FOR THE FRAGILE X-SYNDROME IN SWEDEN
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IDENTIFICATION OF FULL MUTATION FRAGILE-X CARRIERS BY MULTIPLEX PCR OF THE REPEAT SEQUENCES IN THE FMR-1 AND ANDROGEN RECEPTOR GENES
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NONRADIOACTIVE PCR OF THE CGG REPEAT OF THE FRAGILE-X GENE
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FRAGILE X-SYNDROME - DISCORDANT EXPRESSION OF FMR-1 WITH IDENTICAL SMALL CGG INSERTS IN 2 BROTHERS
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MOSAICISM IN FRAGILE-X AFFECTED MALES
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A MENTALLY NORMAL-MALE CARRIER OF A FRAGILE-X FULL MUTATION GAVE BIRTH TO A PREMUTATED DAUGHTER
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MOLECULAR PREDICTORS OF INVOLVEMENT IN FRAGILE-X FEMALES
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FRAGILE-X FULL MUTATION IN 2 CLINICALLY UNAFFECTED BROTHERS
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SINGLE-CELL ANALYSIS OF THE REPEAT EXPANSION MUTATION ASSOCIATED WITH FRAGILE X-SYNDROME
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SCREENING FOR FRAGILE-X MUTATION IN MENTALLY-RETARDED INDIVIDUALS
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TESTING FOR FRAGILE X-SYNDROME IN 120 FAMILIES WITH A HISTORY OF MENTAL-RETARDATION
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AN INDIVIDUAL WITH APPARENT X-LINKED MR AND MOSAICISM OF THE CGG REPEAT REGION IN THE FMR-1 GENE
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A COMPOUND HETEROZYGOTE FEMALE DETECTED IN A FAMILY WITH FRAGILE-X SYNDROME
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UNEXPLAINED FRAGILE X-SYNDROME DNA TEST-RESULTS
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IDENTIFICATION OF THE NUMBER OF THE FRAGILE-X SYNDROME CGG REPEAT USING SILVER STAIN
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Positive fragile X microsatellite associations point to a common mechanism of dynamic mutation evolution
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Decrease in the CGG(n) trinucleotide repeat mutation of the fragile X syndrome to normal size range during paternal transmission
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Predisposition to the fragile X syndrome in Jews of Tunisian descent is due to the absence of AGG interruptions on a rare Mediterranean haplotype
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The fragile X premutation is not a major risk for early menopause.
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Brown VL; Small K; Lakkis L; Wilkinson KD; Warren ST
Purification and characterization of the fragile X mental retardation protein.
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241001593 1997 AMERICAN JOURNAL OF HUMAN GENETICS 61(4):A26-A26
Corbin F; Bouillon M; Rousseau F; Khandjian EW
The fragile-X mental retardation protein is a mRNA chaperone associated with translating complexes.
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Gunter C; Paradee W; Newman J; Sherman SL; Warren ST
A novel biallelic polymorphism in the FMR1 gene shows strong linkage disequilibrium With CGG repeats and flanking microsatellite markers.
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Ju W; Xu WM; Hwang YW; Brown WT; Zhong N
Molecular pathogenetic studies of the fragile X syndrome: Double knockouts of FMR1 and FXR1 affect early development of Xenopus oocytes.
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Hagerman RJ; Staley-Gane L; Linden MG; Tassone F; Hills J; et al.
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Three cases of high functioning fragile X males
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Fragile X chromosome longitudinal sections studied by transmission electron microscopy.
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Paradee W; Rasmussen D; Melikian H; Conn PJ; Warren ST
Hippocampus-independent deficits in the Fragile X mouse.
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Osthus RC; DiMaio MS; Mahoney MJ; Bale AE
Significance of borderline fragile X premutations.
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Feng Y; Absher D; Brown V; Eberhart DE; Malter HE; et al.
FMRP associates with polyribosomes as an mRNP and the I304N mutation causing severe fragile X syndrome abolishes this association.
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Kaufmann WE; Abrams MT; Chen W; Reiss AL
Genotype and molecular phenotype in fragile X syndrome.
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Characterization of new 5 '-(CGG)(n)-3 ' trinucleotide repeat-containing loci in the human genome.
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Sandberg G; Schalling M
Detection of methylated CpG sequences in the FMR-1 promoter using the sodium bisulfite method and expression studies after in vitro methylation and CGG repeat insert.
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Staley-Gane L; Holloway SL; Flynn L; Logan L; Hageman RJ
Assessment of patient agenda prior to genetic counseling for fragile X syndrome.
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de Vries BBA; van den Ouweland AMW; Mohkamsing S; Duivenvoorden HJ; Halley DJJ; et al.
A fragile X screening program in The Netherlands: prevalence of fragile X syndrome lower than previously considered, but the disorder is still underdiagnosed.
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Ashley AE; Robinson H; Glicksman AE; Nolin SL; Schwartz C; et al.
Identification of risk factors associated with instability of the FMR1 CGG repeat.
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Bat O; Kimmel M; Axelrod DE; Chakraborty R
Computer simulation of expansions of DNA triplet repeats in the fragile X syndrome and Huntington's disease.
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Chiurazzi P; Pomponi MG; Willemsen R; Oostra BA; Neri G
In vitro reactivation of the fragile X syndrome gene.
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Correlation and vertical transmission of fragile X syndrome and ovarian failure within a single family.
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Single cell analysis shows different FMR1 CGG repeat stability in sperm and lymphocytes of premutation males.
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Tassone F; Hagerman RJ; Ikle D; Dyer PN; Lampe M; et al.
FMRP expression as a potential prognostic indicator in fragile X syndrome.
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Zhong N; Ju W; Xu WM; Liu B; Dobkin C; et al.
Molecular pathogenetic studies of the fragile X syndrome: A candidate transcript targeted by the fragile X protein FMRP.
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Methylation analysis of the fragile X syndrome by PCR.
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Distribution of apolipoprotein E genotypes in the fragile X syndrome, Batten disease, and Down syndrome populations.
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Sucharov CC; Varandas FR; Rondinelli E; Carakushansky G; Moura-Neto RS
Establishment of a differential diagnostic of patients with Mental Retardation based on Southern-blot and PCR considering the frequency of Fragile X trinucleotide repeats from normal population in Rio de Janeiro, Brazil.
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Taylor AK; Tassone F; Staley-Gane L; Hagerman RJ
Identical premutation size in multiple tissues of a male fragile X carrier.
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Gronskov K; Hjalgrim H; Bjerager MO; BrondumNielsen K
Deletion of all CGG repeats plus flanking sequences in FMR1 does not abolish gene expression
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Kenneson A; Cramer DW; Warren ST
Fragile X premutations are not a major cause of early menopause
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Ashley-Koch AE; Robinson H; Glicksman AE; Nolin SL; Schwartz CE; et al.
Examination of factors associated with instability of the FMR1 CGG repeat
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Noninvasive test for fragile X syndrome, using hair root analysis
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Nolin SL; Houck GE; Gargano AD; Blumstein H; Dobkin CS; et al.
FMR1 CCG-repeat instability by single sperm and lymphocytes of fragile-X premutation males
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Ceman S; Brown V; Warren ST
Isolation of an FMRP-associated mRNP and the identification of nucleolin and the fragile X-related proteins as components of the complex.
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273001802 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A30-A30
Peier AM; McIlwain KL; Paylor R; Nelson DL
FMR1 YAC transgenic mice: rescue of the FMRl knockout mouse and behavior of the CGG trinucleotide repeat.
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Drasinover V; Ehrlich S; Magal N; Taub E; Libman V; et al.
Increased transmission of the premutated allele compared to the normal allele in female carriers of the fragile X syndrome.
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Fisch GS; Howard-Peebles PN; Carpenter N; Tarleton J; Simensen R; et al.
Age-related features of genetic mutations producing cognitive impairment: the Fragile X mutation, NF1, and Williams Syndrome.
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Brown WT; Rabe A; Durnas R; Haubenstock H; Dobkin C
FMR1 knockout mouse shows a strain-specific severe learning impairment: A robust model for the fragile X syndrome.
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277001806 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A105-A105
Kenneson A; Hagedorn CH; Warren ST
Quantitative studies of the fragile X mental retardation 1 (FMR1) gene product, FMRP.
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278001807 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A145-A145
Chernoff EJ; Nunes M; White B; McClellan J; Coll E; et al.
Fragile X premutation status in a male with mental retardation.
00
279001808 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A165-A165
Iqbal MA; Sakati N; Nester A; Ozand P
Cytogenetic diagnosis of fragile X syndrome a study of 305 suspected cases in Saudi Arabia.
00
280001809 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A214-A214
Falik-Zaccai TC; Shachak E; Borochowitz Z; Magal N; Zatz S; et al.
Fragile X syndrome: Population carrier screening and implication for prenatal diagnosis.
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#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
281001810 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A263-A263
Absher DM; Warren SR
Functional studies of mammalian FMRP in yeast.
00
282001811 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A266-A266
Burman RW; Popovich BW; Yates PA; Jacky PB; Schnell JL; et al.
Fully expanded fragile X CGG repeats exhibit a length-and differentiation-dependent instability in cell hybrids that is independent of DNA methylation.
00
283001812 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A268-A268
Crawford DC; Schwartz CE; Warren ST; Sherman SL
Novel repeat structures identified in African-Americans represent a new mechanism leading to fragile X CGG repeat instability.
00
284001813 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A269-A269
DiMarco SP; Ceman S; Torre E; Warren ST
FMRP is a phosphoprotein and a substrate of the Fes non-receptor tryosine kinase.
23
285001814 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A270-A270
El-Hazmi MF
Fragile X mental retardation in syndrome in Saudi Arabia.
00
286001815 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A279-A279
Larsen LA; Armstrong JSM; Gronskov K; Hjalgrim H; Macpherson J; et al.
Haplotype and AGG-interspersion analysis of FMR1(CGG)(n) alleles in the Danish population: Implications for multiple mutational pathways towards fragile X alleles
00
287001816 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A403-A403
Xu B; School JM; Buroker NE; Scott CR; Chen SH
High frequency of the FMR-1 INV10+14c/t polymorphism in Asians, and its association with the Fragile X Syndrome in Caucasians.
01
288001817 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A464-A464
Nolin SL; Houck GE; Gargano AD; Li SY; Glicksman A; et al.
Instability of FMR1 alleles with 40-60 CGG repeats.
00
289001818 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A471-A471
Ventura KA; Fraer LM; Smith EE; Merrill AE; Treat KJ; et al.
Transmission on a fragile X full mutation through a normal transmitting male.
00
290001819 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A474-A474
Lazarou LP; Warburton S; Roberts CE; Lindley VH; Bartlett S; et al.
Fragile X syndrome carrier females with full mutations inherited from a normal transmitting male.
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#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
291001820 1999 AMERICAN JOURNAL OF HUMAN GENETICS 65(4):A493-A493
Tassone F; Hagerman RJ; Taylor AK; Mills JB; Wood S; et al.
FMR1 mRNA expression levels in fragile X.
00
29222401935 2000 AMERICAN JOURNAL OF HUMAN GENETICS 66(1):6-15
Tassone F; Hagerman RJ; Taylor AK; Gane LW; Godfrey TE; et al.
Elevated levels of FMR1 mRNA in carrier males: A new mechanism of involvement in the fragile-X syndrome
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Hundscheid RDL; Sistermans EA; Thomas CMG; Braat DDM; Straatman H; et al.
Imprinting effect in premature ovarian failure confined to paternally inherited fragile X premutations
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29432521937 2000 AMERICAN JOURNAL OF HUMAN GENETICS 66(2):480-493
Crawford DC; Schwartz CE; Meadows KL; Newman JL; Taft LF; et al.
Survey of the fragile X syndrome CGG repeat and the short-tendem-repeat and single-nucleotide-polymorphism haplotypes in an African American population
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295881938 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(1):11-13
Sherman SL
Premature ovarian failure among fragile X premutation carriers: Parent-of-origin effect?
48
296241939 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(1):253-254
Murray A; Ennis S; Morton N
No evidence for parent of origin influencing premature ovarian failure in fragile X premutation carriers
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297681940 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(1):254-255
Vianna-Morgante AM; Costa SS
Premature ovarian failure is associated with maternally and paternally inherited premutation in Brazilian families with fragile X
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298331941 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(1):256-258
Hundscheid RDL; Thomas CMG; Braat DDM; Oostra BA; Smits APT
Premature ovarian failure is associated with maternally and paternally inherited premutation in Brazilian families with fragile X - Reply
25
299001942 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):18-18
Jin P; Feng Y; Brown V; Warren ST
Identification of polyribosomes-associated mRNAs regulated by fragile X mental retardation protein (FMRP) using oligonucleotide microarrays.
12
300001943 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):18-18
Brown V; Ceman S; Jin P; Jin C; Wilkinson KD; et al.
Messenger RNAs associated with the fragile X mental retardation protein in mouse brain.
11

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