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Mon Apr 4 11:09:44 2005
Papers with one of the following phrases in the title:
fragile x or FMRP or trinucleotitde expansion or nucleotide expansion or cgg

Nodes: 2647, Authors: 5321, Journals: 428, Outer References: 16458, Words: 3536
Collection span: 1967 - 2005
View: Overview. Sorted by journal name.
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#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
301001944 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):25-25
Crawford DC; Wilson B; Sherman SL
Factors involved in the initial mutation of the fragile X CGG repeat as determined by sperm small pool-PCR.
00
302001945 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):26-26
Hagerman RJ; Tassone F; Leehey M; Hills J; Wilson R; et al.
Cerebellar tremor and cerebellar cortical atrophy in older males with the fragile X premutation.
00
303001946 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):50-50
Neri G; Pomponi MG; Pietrobono R; Chiurazzi P; Oostra BA
Differential reactivation of the FMR1 gene in fragile X patients cell lines.
00
304001947 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):50-50
Kenneson A; Zhang F; Warren ST
Fragile X premutation alleles are associated with reduced FMRP levels due to a reduction of message translatability.
00
305001948 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):57-57
Li MM; Nelson L; Bamshad M; Ward K
Fragile X mosaics in a family with multiple mildly affected individuals.
00
306001949 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):130-130
Khalifa M; Struthers J
High frequency of Klinefelter syndrome among a large population of patients referred for Fragile X syndrome testing due to undiagnosed mental retardation.
00
307001950 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):135-135
Harris SW; Brown KE; Hills JL; Tassone F; Hagerman PJ; et al.
Adaptive functioning and molecular relationships in individuals with fragile X syndrome.
00
308001951 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):184-184
Tassone F; Hagerman RJ; Taylor AK; Hagerman PJ
Clinical and molecular correlations in individuals with a fragile X full mutation.
00
309001952 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):200-200
Ceman SS; Kenneson A; Nelson R; Jin C; Lakkis L; et al.
Development and characterization of a unique set of anti-FMRP antibodies using a novel strategy.
00
310001953 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):236-236
Mathews DJ; Hudson R; Eichier E; Chakravarti A
Sequence variation and linkage disequilibrium at the fragile X syndrome locus.
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
311001954 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):238-238
Sullivan AK; Crawford DC; Meadows KL; Wilson B; Sherman SL
Parent-child transmission of intermediate FMR1 CGG repeat alleles: Examination of factors associated with repeat instability.
00
312001955 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):247-247
Brown NM; Friez MJ; Longshore JW; Stenzel TT
Evaluation of an automated commercially available PCR kit for determination of Fragile X (FRAXA) normal, gray-zone and premutation allele sizes.
00
313001956 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):248-248
Murphy KM; Nunes ME
Comparison of child-only versus mother/child sample collection in Fragile X testing.
00
314001957 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):254-254
Weinhaeusel A; Skarits C; Haas OA
Methylation-sensitive PCR (MS-PCR) analysis of the fragile X (FRAXA) syndrome.
00
315001958 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):348-348
Dyack S; Steele L; Koultchitski G; Yang Y; Weksberg R; et al.
AGG interruptions in the CGG trinucleotide repeat tract of the FMR1 gene may contribute to stability of Fragile X premutations.
00
316001959 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):360-360
Ramos FJ; Mila M; Ortilles M; Rife M; Tazon B; et al.
Validity of the analysis of the FMRP expression in bloodsmears as a screening method for the Fragile X Syndrome.
11
317001960 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):364-364
Chen SH; Xu B; Shoof JM; Buroker NE; Scott CR
Evidence for a stepwise expansion of the CGG repeats within the FMR1 gene.
00
318001961 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):365-365
Nolin SL; Rousseau F; Houck GE; Gargano AD; Biancalana V; et al.
FMR1 CGG expansion to full mutation: What is the lower limit in premutation females?
00
319001962 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):365-365
O'Donnell WT; Warren ST
Investigating the cause of macroorchidism in fragile X syndrome using oligonucleotide microarrays.
00
320001963 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):366-366
Raca G; Siyanova E; Mirkin S
Janus effects of premutation size CGG repeats on gene expression.
11
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
321001964 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):366-366
Parades WJ; Warren ST
Meiotic stability of a fragile X premutation CGG trinucleotide repeat in a mouse model.
00
322001965 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):415-415
Najmabadi H; Taghizadeh F; Teimourian SH; Karimi-Nejad R; Shafeghati Y; et al.
Molecular analysis of Fragile X syndrome in Iranian population.
00
323001966 2000 AMERICAN JOURNAL OF HUMAN GENETICS 67(4):428-428
Brown WT; Ding X; Idrissi AE; Scalia J; Glicksman A; et al.
Fragile X transgene and embryonic lethality in mice.
00
32429402094 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(2):351-360
Toledano-Alhadef H; Basel-Vanagaite L; Magal N; Davidov B; Ehrlich S; et al.
Fragile-X carrier screening and the prevalence of premutation and full-mutation carriers in Israel
1322
32521342095 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(3):504-515
Wohrle D; Salat U; Hameister H; Vogel W; Steinbach P
Demethylation, reactivation, and destabilization of human fragile X full-mutation alleles in mouse embryocarcinoma cells
410
326002096 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):177-177
Hagerman RJ; Greco C; Chudley A; Leehey M; Tassone F; et al.
Neuropathology and neurodegenerative features in some older male premutation carriers of fragile X syndrome.
34
327002097 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):291-291
Thiele H; Peters H; Bahrke D; Hansmann I
Homozygosity for a premutation of the FMR1 gene and normal phenotype in two sisters from a family with fragile X syndrome.
00
328002098 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):352-352
Gantois I; Reyniers E; Kooy RF
Identification of genes differentially expressed in the fragile X syndrome.
00
329002099 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):372-372
Naumann F; Muller-Hartmann H; Deissler H; Doerfler W
Functional studies on the human 5 '-CGG-3 '-binding protein CGGBP1 (p20).
00
330002100 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):372-372
Neri G; Pomponi MG; Pietrobono R; Chiurazzi P
Pharmacological reactivation of the FMR1 gene of the fragile X syndrome.
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
331002101 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):430-430
Jakupciak JP; O'Connell CD; Atha DA; Richie KL
Standardization of PCR amplification for fragile X trinucleotide repeat measurements.
00
332002102 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):431-431
Jenkins EC; Li SY; Yao XL; Lanter S; Sudhalter V; et al.
Detecting mosaic FMR-1 (fragile X) mutations: Southern blotting versus monoclonal antibody analysis.
00
333002103 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):436-436
Patel ZM; Menon SR; D'souza AK; Adhia RA; Sanghavi DA; et al.
Validity of the analysis of FMRP expression in blood smears as a screening method for the fragile X syndrome in Indian population.
00
334002104 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):438-438
Zhou Y; Chong SS
Simplified molecular diagnostic testing for fragile X syndrome using methylation-specific PCR (ms-PCR).
00
335002105 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):554-554
Heine-Sur D; Pico G; Torres-Juan L; Bernues M; Iglesias J; et al.
A female with Fragile-X shows an affected male-like phenotype and skewed inactivation of the functional chromosome.
00
336002106 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):585-585
Essop FB; Greenberg J; Basel D; Krause A
Molecular analysis of a fragile X family with two females homozygous for a premutation.
00
337002107 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):586-586
Nolin SL; Houck GE; Gargano AD; Brown WT
Large fragile X premutatin alleles may often contain two AGG Interruptions.
00
338002108 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):635-635
Dobkin CS; Ding X; Brown WT; El Idrissi A
Reduced hippocampal GABAa receptors and increased kainic acid seizure susceptibility in the fragile X mouse.
00
339002109 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):667-667
Brown WT; Nolin S; Houck GE; Ding XH; Glicksman A; et al.
The Fragile X Syndrome: Screening and prenatal diagnosis.
00
340002110 2001 AMERICAN JOURNAL OF HUMAN GENETICS 69(4):669-669
Mallolas J; Badenas C; Rite M; Soler A; Borrell A; et al.
Prospective study of molecular fragile X syndrome prenatal diagnosis.
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
341002217 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):175-175
Jin P; Zhang F; Zarnescu DC; Moses K; Lucchesi JC; et al.
A Drosophila model of fragile X premutation: CGG repeat instability and dominant-negative effects of premutation riboCGG repeat.
00
342002218 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):185-185
Jacquemont S; Hagerman RJ; Leehey M; Greco C; Brunberg J; et al.
Characterization of a progressive neurological condition in older adult male carriers of the fragile X premutation.
22
343002219 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):259-259
Hagerman PJ; Greco CM; Hagerman RJ; Tassone F; Chudley AE; et al.
Neuronal intranuclear inclusions in a tremor/ataxia syndrome among fragile X premutation carriers.
00
344002220 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):270-270
Griffin KJ; Bei T; Meck J; Wong LJ; Bondy C; et al.
Gender ambiguity and fragile X: a new syndrome.
00
345002221 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):287-287
Hagerman R; Goodlin-Jones BL; Spence S; Albrect L; Bacalman S; et al.
The fragile X premutation and autistic spectrum disorders.
00
346002222 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):288-288
Harris SW; Goodlin-Jones BL; Bacalman S; Jardini T; Rao S; et al.
Fragile X and autism diagnosis by two standard methodologies.
00
347002223 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):331-331
Tassone F; Sahota P; Pleasant N; Laird C; Hagerman P
Methylation analysis of the promoter region in fragile X males with hypermethylated, full mutation alleles
00
348002224 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):338-338
Naumann F; Schmitz B; Doerfler W
Expression of the human and murine 5 '-(CGG)(n)-3 '-binding proteins CGGBP1.
00
349002225 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):347-347
Brown WT; Nolin SL; Dobkin CS; Houck GS; Glicksman A; et al.
Frequency of fragile X in multiplex autism: Testing the AGRE families.
00
350002226 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):373-373
Ennis S; Brightwell G; Collins A; Jacobs P; Morton NE
Phylogeny of fragile X haplotypes from an English population.
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
351002227 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):377-377
Zabala WM; Nava N; Gonzalez S; Delgado W; Borjas L; et al.
Clinical and molecular analysis of the fragile X syndrome in mentally retarded males from the Venezuelan northwestern region.
00
352002228 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):384-384
Chen S; Schoof JM; Lemoine CJ; Gordon CL; Scott CR
Prevalence survey of the Fragile X E syndrome referred for Fragile X syndrome testing in boys with mental retardation.
00
353002229 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):505-505
Dobkin CS; Ding XH; Houck GE; Mitchell E; Brown WT; et al.
A rare Eag I polymorphism that may confound fragile X diagnosis.
00
354002230 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):507-507
Neri G; Tabolacci E; Pietrobono R; Pomponi MG; Chiurazzi P
Histone hyperacetylation and reactivation of the fragile X syndrome gene.
01
355002231 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):518-518
Maranduba CMC; Vianna-Morgante AM; Passos-Bueno MR
P172H mutation in the TM4SF2 gene accounts for 1% of non-fragile X mental retardation in Brazilian patients.
00
356002232 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):523-523
Bastaki LA; Al-Awadi SA; Hegazi FA; Turky NA; Mustafa MA; et al.
PCR technique and significance in fragile X syndrome.
00
35710372233 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):923-932
Coffee B; Zhang FP; Ceman S; Warren ST; Reines D
Histone modifications depict an aberrantly heterochromatinized FMR1 gene in fragile X syndrome
314
35832392348 2003 AMERICAN JOURNAL OF HUMAN GENETICS 72(2):454-464
Nolin SL; Brown WT; Glicksman A; Houck GE; Gargano AD; et al.
Expansion of the fragile X CGG repeat in females with premutation or intermediate alleles
1321
35919362349 2003 AMERICAN JOURNAL OF HUMAN GENETICS 72(4):869-878
Jacquemont S; Hagerman RJ; Leehey M; Grigsby J; Zhang L; et al.
Fragile X premutation tremor/ataxia syndrome: Molecular, clinical, and neuroimaging correlates
2644
360002350 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):162-162
Jin P; Ceman S; Zarnescu DC; Nakamoto M; Mowrey J; et al.
Biochemical and genetic interaction between the fragile X mental retardation protein and the microRNA pathway.
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
361002351 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):163-163
Allen E; Letz R; Sherman S
Association of FMR1 CGG repeat size, X-inactivation ratio and transcript level with cognitive performance among women.
00
362002352 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):163-163
Cronister A; Teicher J; Custer T; Rohlfs EM
Prevalence of premutation and intermediate alleles among patients referred for fragile X carrier testing.
00
363002353 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):163-163
Jiang Y; Wakui K; Liu Q; Kashork CD; Lehoczky J; et al.
A fragile X mental retardation protein interacting protein maps to the proximal breakpoint of the Prader-Willi syndrome common deletion region.
00
364002354 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):163-163
Jacquemont S; Hagerman RJ; Leehey MA; Hall DA; Levine RA; et al.
Penetrance of the fragile X-associated tremor/ataxia syndrome (FXTAS) in a premutation carrier population: Initial results from a California family-based study.
00
365002355 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):266-266
Hagerman RJ; Jacquemont S; Tassone F; Greco C; Brunberg J; et al.
Fragile X-associated tremor/ataxia syndrome (FXTAS) involvement in females
00
366002356 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):296-296
Harris SW; Tassone F; Barbato I; Hagerman RJ
FMRP, FMR1-mRNA, and psychopathology correlations in women with the fragile X premutation.
00
367002357 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):314-314
Medne L; Russell K; Ming J; Krantz ID; Souders M; et al.
Subtelomeric FISH analysis in 108 autistic patients as adjunct to chromosome analysis and fragile X testing
00
368002358 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):330-330
Herman K; Nowicki S; Tassone F; Koldewyn K; Bacalman S; et al.
Correlations between DNA, FMRP, and mRNA levels and ADOS-G and ADI-R scores in patients with Fragile X Syndrome.
00
369002359 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):337-337
Nolin SL; Houck GE; Glicksman A; Gargano AD; Brown WT
Large fragile X premutation alleles may often contain two AGG interruptions.
00
370002360 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):348-348
Tabolacci E; Pietrobono R; Chiurazzi P; Neri G
Variation of histone acetylation/methylation in the FMR1 gene of the fragile X syndrome following pharmacological reactivation.
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
371002361 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):348-348
O'Donnell WT; Ceman S; Warren ST
Phosphorylation of the fragile X mental retardation protein regulates translation of its mRNA ligands.
00
372002362 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):372-372
Reddy K
Autism: Incidence of cytogenetic abnormality and fragile-X syndrome.
00
373002363 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):377-377
Ennis S; Collins A; Morton NE
The use of SNP-based haplotypes and LD blocks to positionally clone modifying determinants of expansion of the Fragile X triplet repeat
00
374002364 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):383-383
Rigby AS; Turk J; Mills AC; James N; Hollis C; et al.
Social functioning in male premutation carriers of Fragile X (FRAX) syndrome
00
375002365 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):457-457
Mirakhory M; Aleyassin A
Study of folic acid pathway genes alteration in fragile X syndrome.
00
376002366 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):555-555
Di Maria E; Grasso M; Pigullo S; Faravelli F; Abbruzzese G; et al.
Further evidence that a tremor/ataxia syndrome may occur in Fragile X premutation carriers: findings from two clinical series.
00
377002367 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):557-557
Gantois I; Vandesompele J; Speleman F; D'Hooge R; Severijnen LA; et al.
Expression profiling reveals involvement of the GABA(A) receptor subunit delta in the fragile X syndrome.
00
378002368 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):573-573
Wronska A; Ju W; Brown WT; Zhong N
Studies of FMRP-binding RNAs with a yeast tri-hybrid system.
00
379002369 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):585-585
Fan H; Booker JK; McCandless SE; Shashi V; Farber RA
Mosaicism for FMR1 gene full mutation and deletion in a fragile X female.
00
380002370 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):586-586
Greco CM; Tassone F; Jaquemont S; Hagerman RJ; Sahota PK; et al.
Intranuclear neuronal inclusions in two female carriers of the fragile X premutation
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
381002371 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):587-587
Tassone F; Hagerman RJ; Garcia D; Sahota PK; Khandjian EW; et al.
Intranuclear inclusions in fragile X-associated tremor/ataxia syndrome neuronal cells from five premutation carriers.
00
382002372 2003 AMERICAN JOURNAL OF HUMAN GENETICS 73(5):589-589
Chen LS; Tassone F; Sahota P; Hagerman PJ
The (CGG)(n) repeat elements within the 5 ' untranslated region of the FMR1 message provides both positive and negative cis effects on in vivo translation of a downstream reporter.
00
38341802480 2004 AMERICAN JOURNAL OF HUMAN GENETICS 74(5):805-816
Hagerman PJ; Hagerman RJ
The fragile-X premutation: A maturing perspective
814
38415262481 2004 AMERICAN JOURNAL OF HUMAN GENETICS 74(5):1051-1056
Hagerman RJ; Leavitt BR; Farzin F; Jacquemont S; Greco CM; et al.
Fragile-X-associated tremor/ataxia syndrome (FXTAS) in females with the FMR1 premutation
37
385112482 2004 AMERICAN JOURNAL OF HUMAN GENETICS 75(2):352-352
Hagerman; Hagerman
The fragile-X premutation: A maturing perspective (vol 74, pg 805, 2003)
00
3862102483 2004 AMERICAN JOURNAL OF HUMAN GENETICS 75(4):730-731
Mandel JL
Comparative frequency of fragile-X (FMR1) and creatine transporter (SLC6A8) mutations in X-linked mental retardation
11
387152484 2004 AMERICAN JOURNAL OF HUMAN GENETICS 75(4):731-732
Salomons GS; Ropers HH
Comparative frequency of fragile-X (FMR1) and creatine transporter (SLC6A8) mutations in X-linked mental retardation - Reply
00
38818412620 2005 AMERICAN JOURNAL OF HUMAN GENETICS 76(2):302-311
Edamura KN; Leonard MR; Pearson CE
Role of replication and CpG methylation in fragile X syndrome CGG deletions in primate cells
00
389066 1980 AMERICAN JOURNAL OF MEDICAL GENETICS 7(4):503-505
KAISERMCCAW B; HECHT F; CADIEN JD; MOORE BC
FRAGILE X-LINKED MENTAL-RETARDATION
1422
3900050 1982 AMERICAN JOURNAL OF MEDICAL GENETICS 11(4):489-495
HECHT F; JACKY PB; SUTHERLAND GR
THE FRAGILE X-CHROMOSOME - CURRENT METHODS
1635
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
39112051 1982 AMERICAN JOURNAL OF MEDICAL GENETICS 13(2):139-148
BROOKWELL R; DANIEL A; TURNER G; FISHBURN J
THE FRAGILE X(Q27) FORM OF X-LINKED MENTAL-RETARDATION - FUDR AS AN INDUCING AGENT FOR FRA(X)(Q27) EXPRESSION IN LYMPHOCYTES, FIBROBLASTS, AND AMNIOCYTES
2449
392832108 1983 AMERICAN JOURNAL OF MEDICAL GENETICS 14(4):699-712
CHUDLEY AE; KNOLL J; GERRARD JW; SHEPEL L; MCGAHEY E; et al.
FRAGILE (X) X-LINKED MENTAL-RETARDATION .1. RELATIONSHIP BETWEEN AGE AND INTELLIGENCE AND THE FREQUENCY OF EXPRESSION OF FRAGILE (X)(Q28)
5680
39345109 1983 AMERICAN JOURNAL OF MEDICAL GENETICS 14(4):795-796
DAKER MG
FRAGILE X-CHROMOSOME IN NORMAL MALES
24
39411110 1983 AMERICAN JOURNAL OF MEDICAL GENETICS 14(4):797-797
HECHT F; JACKY PB; SUTHERLAND GR
FRAGILE X-CHROMOSOME IN NORMAL MALES - REPLY
12
395228111 1983 AMERICAN JOURNAL OF MEDICAL GENETICS 15(1):113-119
FILIPPI G; RINALDI A; ARCHIDIACONO N; ROCCHI M; BALAZS I; et al.
LINKAGE BETWEEN G6PD AND FRAGILE-X SYNDROME
1943
396114112 1983 AMERICAN JOURNAL OF MEDICAL GENETICS 15(4):631-635
HOWARDPEEBLES PN; FINLEY WH
SCREENING OF MENTALLY-RETARDED MALES FOR MACRO-ORCHIDISM AND THE FRAGILE-X CHROMOSOME
1622
397103406172 1984 AMERICAN JOURNAL OF MEDICAL GENETICS 17(1):5-94
OPITZ JM; SUTHERLAND GR
CONFERENCE REPORT - INTERNATIONAL WORKSHOP ON THE FRAGILE-X AND X-LINKED MENTAL-RETARDATION
52116
398416173 1984 AMERICAN JOURNAL OF MEDICAL GENETICS 17(1):111-121
HAGERMAN RJ; VANHOUSEN K; SMITH ACM; MCGAVRAN L
CONSIDERATION OF CONNECTIVE-TISSUE DYSFUNCTION IN THE FRAGILE-X SYNDROME
2535
399112174 1984 AMERICAN JOURNAL OF MEDICAL GENETICS 17(1):123-131
HAGERMAN RJ; SYNHORST DP
MITRAL-VALVE PROLAPSE AND AORTIC DILATATION IN THE FRAGILE-X SYNDROME
917
400216175 1984 AMERICAN JOURNAL OF MEDICAL GENETICS 17(1):159-174
MERYASH DL; CRONK CE; SACHS B; GERALD PS
AN ANTHROPOMETRIC STUDY OF MALES WITH THE FRAGILE-X SYNDROME
2643
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
401429176 1984 AMERICAN JOURNAL OF MEDICAL GENETICS 17(1):175-194
PARTINGTON MW
THE FRAGILE-X SYNDROME .2. PRELIMINARY DATA ON GROWTH AND DEVELOPMENT IN MALES
5265
402325177 1984 AMERICAN JOURNAL OF MEDICAL GENETICS 17(1):195-207
SIMPSON NE; NEWMAN BJ; PARTINGTON MW
FRAGILE-X SYNDROME .3. DERMATOGLYPHIC STUDIES IN MALES
1016
40304178 1984 AMERICAN JOURNAL OF MEDICAL GENETICS 17(1):209-214
RHOADS FA
FRAGILE-X SYNDROME IN HAWAII - A SUMMARY OF CLINICAL-EXPERIENCE
1221
4041043179 1984 AMERICAN JOURNAL OF MEDICAL GENETICS 17(1):215-239
JENKINS EC; BROWN WT; BROOKS J; DUNCAN CJ; RUDELLI RD; et al.
EXPERIENCE WITH PRENATAL FRAGILE-X DETECTION
3544
405416180 1984 AMERICAN JOURNAL OF MEDICAL GENETICS 17(1):241-252
SOUDEK D; PARTINGTON MW; LAWSON JS
THE FRAGILE-X SYNDROME .1. FAMILIAL VARIATION IN THE PROPORTION OF LYMPHOCYTES WITH THE FRAGILE SITE IN MALES
2429
40602181 1984 AMERICAN JOURNAL OF MEDICAL GENETICS 17(1):253-254
DEV VG; MIXON C
5-AZACYTIDINE DECREASES THE FREQUENCY OF FRAGILE-X EXPRESSION IN PERIPHERAL LYMPHOCYTE CULTURE
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FRAGILE-X EXPRESSION SUPPRESSED IN EITHER FUDR OR METHOTREXATE TREATED FIBROBLASTS BY PRETREATMENT WITH 5-AZACYTIDINE
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THE FRAGILE-X SYNDROME .4. PROGRESS TOWARDS THE IDENTIFICATION OF LINKED RESTRICTION FRAGMENT LENGTH VARIANTS (RFLVS)
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RECOMBINATION BETWEEN THE FRAGILE-X AND G6PD
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FOLIC-ACID THERAPY IN THE FRAGILE-X SYNDROME
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FOLIC-ACID THERAPY IN THE FRAGILE-X SYNDROME
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FOLATE METABOLISM IN CELLS FROM FRAGILE-X SYNDROME PATIENTS AND CARRIERS
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FRAGILE-X MALES WITH NORMAL INTELLIGENCE - AND IF SO, WHY
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FRAGILE-X MALES WITH NORMAL INTELLIGENCE - AND IF SO, WHY - REPLY
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DANIEL A; EKBLOM L; PHILLIPS S
CONSTITUTIVE FRAGILE SITES 1P31, 3P14, 6Q26, AND 16Q23 AND THEIR USE AS CONTROLS FOR FALSE-NEGATIVE RESULTS WITH THE FRAGILE(X)
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WANG JCC; BEARDSLEY GP; ERBE RW
ANTIFOLATE-INDUCED MISINCORPORATION OF DEOXYURIDINE MONOPHOSPHATE INTO DNA BY CELLS FROM PATIENTS WITH THE FRAGILE-X SYNDROME
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PEMBREY ME; WINTER RM; DAVIES KE
A PRE-MUTATION THAT GENERATES A DEFECT AT CROSSING OVER EXPLAINS THE INHERITANCE OF FRAGILE X MENTAL RETARDATION
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REDUCTION OF FRAGILE X-EXPRESSION IN BLOOD AFTER CRYOPRESERVATION
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FRAGILE-X AND MARTIN-BELL SYNDROME - NEW SOURCE OF INFORMATION
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NEUROFIBROMATOSIS AND FRAGILE-X SYNDROME IN THE SAME PATIENT
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CONFERENCE REPORT - 2ND INTERNATIONAL WORKSHOP ON THE FRAGILE-X AND ON X-LINKED MENTAL-RETARDATION
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FEMALE RELATIVES IN FAMILIES WITH THE FRAGILE X-SYNDROME
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THE FEMALE AND THE FRAGILE-X - A STUDY OF 144 OBLIGATE FEMALE CARRIERS
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SIMPSON NE
DERMATOGLYPHIC INDEXES OF MALES WITH THE FRAGILE-X SYNDROME AND OF THE FEMALE HETEROZYGOTES
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ORAL FINDINGS IN FRAGILE-X SYNDROME
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AORTIC ROOT DILATATION AND MITRAL-VALVE PROLAPSE IN THE FRAGILE-X SYNDROME
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SPEECH DISTURBANCES (CLUTTERING) IN MILDLY IMPAIRED MALES WITH THE MARTIN-BELL FRAGILE-X SYNDROME
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BRIEF CLINICAL REPORT - METAPHYSEAL DYSOSTOSIS AND CONGENITAL NYSTAGMUS IN A MALE INFANT WITH THE FRAGILE-X SYNDROME
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GONADAL-FUNCTION IN MEN WITH THE MARTIN-BELL (FRAGILE-X) SYNDROME
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ORAL FOLIC-ACID VERSUS PLACEBO IN THE TREATMENT OF MALES WITH THE FRAGILE-X SYNDROME
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HIGH-DOSE FOLIC-ACID TREATMENT OF FRAGILE-(X) MALES
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FOLIC-ACID TREATMENT IN MALES AND FEMALES WITH FRAGILE-(X)-SYNDROME
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ASSESSMENT OF BEHAVIOR-CHANGE IN A FRAGILE-X SYNDROME MALE TREATED WITH FOLIC-ACID
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THE PRENATAL DETECTION OF THE FRAGILE-X CHROMOSOME - REVIEW OF RECENT EXPERIENCE
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2ND TRIMESTER PRENATAL-DIAGNOSIS OF THE FRAGILE-X
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FRAGILE-X AND AUTISM - A MULTICENTER SURVEY
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INFANTILE-AUTISM - AN OCCASIONAL MANIFESTATION OF FRAGILE-(X) MENTAL-RETARDATION
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AN ANALYSIS OF AUTISM IN 50 MALES WITH THE FRAGILE-X SYNDROME
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AUTISM IN FRAGILE-X FEMALES
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INFANTILE-AUTISM AND THE FRAGILE-X - A SWEDISH MULTICENTER STUDY
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SOMATIC-CELL HYBRID STUDIES OF FRAGILE-(X) EXPRESSION IN A CARRIER FEMALE AND TRANSMITTING MALE
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CAFFEINE ENHANCES FRAGILE-(X) EXPRESSION IN SOMATIC-CELL HYBRIDS
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FRAGILE-X EXPRESSION INCREASED BY LOW CELL-CULTURE DENSITY
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METHIONINE METABOLISM AND FRAGILE-X EXPRESSION
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FRAGILE-X - CARRIER DETECTION IN PREGNANCY
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SEX-CHROMOSOME ANEUPLOIDY IN FRAGILE-X CARRIERS
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UCHIDA IA; FREEMAN VCP; BASRUR PK
THE FRAGILE-X IN CATTLE
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JACOBS PA; MAYER M; ABRUZZO MA
STUDIES OF THE FRAGILE (X) SYNDROME IN POPULATIONS OF MENTALLY-RETARDED INDIVIDUALS IN HAWAII
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PREVALENCE OF THE FRAGILE-X SYNDROME IN MENTALLY-RETARDED BOYS IN A SWEDISH COUNTY
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FRAGILE-X MENTAL-RETARDATION - PREVALENCE IN A GROUP OF INSTITUTIONALIZED PATIENTS IN ITALY AND DESCRIPTION OF A NOVEL EEG PATTERN
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JACOBS PA; SHERMAN S; TURNER G; WEBB T
THE FRAGILE(X) SYNDROME - THE MUTATION PROBLEM
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BROWN WT; GROSS AC; CHAN CB; JENKINS EC
DNA LINKAGE STUDIES IN THE FRAGILE-X SYNDROME SUGGEST GENETIC-HETEROGENEITY
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HOEGERMAN SF; RARY JM
SPECULATION ON THE ROLE OF TRANSPOSABLE ELEMENTS IN HUMAN GENETIC-DISEASE WITH PARTICULAR ATTENTION TO ACHONDROPLASIA AND THE FRAGILE-X SYNDROME
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INHERITANCE OF FRAGILE-X SYNDROME - AN HYPOTHESIS
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VANDYKE DL; WEISS L
MATERNAL EFFECT ON INTELLIGENCE IN FRAGILE-X MALES AND FEMALES
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DAR H; BAREL H; JAFFE M; WINTER ST
THE FRAGILE-X SYNDROME - THE DILEMMA OF SELECTING PATIENTS FOR EXAMINATION
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SHABTAI F; KLAR D; HART J; HALBRECHT I
FRAGILE-X SYNDROME - A GENETIC OR AN INFECTIOUS-DISEASE
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WENGER SL; HENNESSEY JC; STEELE MW
INCREASED SISTER CHROMATID EXCHANGE FREQUENCY AT XQ27-SITE IN AFFECTED FRAGILE-X MALES
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MULLEY JC; SUTHERLAND GR
FRAGILE-X TRANSMISSION AND THE DETERMINATION OF CARRIER PROBABILITIES FOR GENETIC-COUNSELING
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PHENOTYPIC VARIATION IN MALE-TRANSMITTED FRAGILE-X - GENETIC INFERENCES
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MULLEY JC; GEDEON AK; THORN KA; BATES LJ; SUTHERLAND GR
LINKAGE AND GENETIC-COUNSELING FOR THE FRAGILE-X USING DNA PROBE-52A, PROBE-F9, PROBE-DX13, AND PROBE-ST14
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CARPENTER NJ; VEENEMA H; BAKKER E; HOFKER MH; PEARSON PL
A NEW DNA PROBE PROXIMAL TO AND CLOSELY LINKED TO FRAGILE-X
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COGNITIVE VARIABILITY IN THE FRAGILE X-SYNDROME
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CONFERENCE REPORT - 3RD INTERNATIONAL WORKSHOP ON THE FRAGILE-X AND X-LINKED MENTAL-RETARDATION
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PREVALENCE OF THE FRAGILE-X OR MARTIN-BELL SYNDROME
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THE DISTRIBUTION OF FRAGILE-X CHROMOSOMES IN AMNIOTIC CELLS CULTURED BY THE INSITU TECHNIQUE
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HIGH-LEVELS OF FRAGILE-X EXPRESSION IN NORMAL MALES INDUCED BY APHIDICOLIN
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THE FRAGILE-X SYNDROME IN NORTHERN FINLAND - A GENEALOGIC STUDY
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FURTHER NEUROPATHOLOGICAL OBSERVATIONS IN ADULT FRAGILE-X
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UNSUSPECTED PRENATAL-DIAGNOSIS OF THE FRAGILE-X
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IDENTICAL EXPRESSION OF THE FRAGILE-X BUT DISCORDANT CLINICAL MANIFESTATIONS IN MONOZYGOTIC TWINS WITH MARTIN-BELL SYNDROME
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THE PROS AND CONS OF PREVENTIVE SCREENING FOR THE FRAGILE (X)
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BIBLIOGRAPHY ON X-LINKED MENTAL-RETARDATION, THE FRAGILE-X AND RELATED SUBJECTS-IV (1988)
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FRAGILE-X SYNDROME AND NEOPLASIA
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AORTIC HYPOPLASIA AND CARDIAC VALVULAR ABNORMALITIES IN A BOY WITH FRAGILE-X SYNDROME
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FRAGILE-X MUTATION AND KLINEFELTER SYNDROME - A REAPPRAISAL
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THE CONCURRENCE OF KLINEFELTER SYNDROME AND FRAGILE-X SYNDROME
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ANEUPLOIDY AND THE FRAGILE-X SYNDROME
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FRAGILE-X SYNDROME - GROWTH, DEVELOPMENT, AND INTELLECTUAL FUNCTION
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GROWTH-PATTERN IN BOYS WITH FRAGILE-X
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PHOTOANTHROPOMETRIC ANALYSIS OF INDIVIDUALS WITH THE FRAGILE-X SYNDROME
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A DERMATOGLYPHIC STUDY OF A GROUP OF SICILIAN CHILDREN WITH FRAGILE-X SYNDROME
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KEMPER MB; HAGERMAN RJ; ALTSHULSTARK D
COGNITIVE PROFILES OF BOYS WITH THE FRAGILE-X SYNDROME
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BROWN WT; RUDELLI RD; WISNIEWSKI HM
FRAGILE-X SYNDROME - NEUROPATHOLOGY CENTER
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VARIABLE EXPRESSION OF THE FRAGILE-X SYNDROME IN HETEROZYGOUS FEMALES OF NORMAL INTELLIGENCE
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HOWARDPEEBLES PN; BROWN WT
THE FRAGILE-X SYNDROME - VARIABILITY OF EXPRESSION IN CARRIER FEMALES
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SUTHERS GK; TURNER G; MULLEY JC
CASE-REPORT - FRAGILE-X SYNDROME AND NEPHROGENIC DIABETES-INSIPIDUS
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AUTISM AND THE FRAGILE-X SYNDROME
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PURVISSMITH SG; LAING S; SUTHERLAND GR; BAKER E
PRENATAL-DIAGNOSIS OF THE FRAGILE-X - THE AUSTRALASIAN EXPERIENCE
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SHAPIRO LR; WILMOT PL; MURPHY PD; BREG WR
EXPERIENCE WITH MULTIPLE APPROACHES TO THE PRENATAL-DIAGNOSIS OF THE FRAGILE-X SYNDROME - AMNIOTIC-FLUID, CHORIONIC VILLI, FETAL BLOOD AND MOLECULAR METHODS
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PRENATAL-DIAGNOSIS OF FRAGILE-X SYNDROME BY PLACENTAL (CHORIONIC VILLI) BIOPSY CULTURE
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SANFILIPPO S; RAGUSA RM; SCILLATO F; RUGGERI M; NERI G
FRAGILE-X EXPRESSION IN NORMAL AND MENTALLY-RETARDED SUBJECTS - EFFECT OF TREATMENT WITH AN ANTIFOLIC AGENT
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HAGERMAN RJ; MURPHY MA; WITTENBERGER MD
A CONTROLLED TRIAL OF STIMULANT MEDICATION IN CHILDREN WITH THE FRAGILE-X SYNDROME
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FISCH GS; COHEN IL; GROSS AC; JENKINS V; JENKINS EC; et al.
FOLIC-ACID TREATMENT OF FRAGILE-X MALES - A FURTHER STUDY
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FRYNS JP; VANDENBERGHE H
INACTIVATION PATTERN OF THE FRAGILE-X IN HETEROZYGOUS CARRIERS
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TOMMERUP N; LAING S; CHRISTENSEN IJ; TURNER G
SCREENING FOR THE FRAGILE-X - HOW MANY CELLS SHOULD WE ANALYZE
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TURNER G; PARTINGTON MW
FRAGILE(X) EXPRESSION, AGE AND THE DEGREE OF INTELLECTUAL HANDICAP IN THE MALE
45
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KRAWCZUN MS; JENKINS EC; BROWN WT; SILVERMAN WP
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INSITU NICK TRANSLATION OF THE FRAGILE-X REGION
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FRAGILE-X TESTING IN MOTHERS OF TRANSMITTING MALES
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FRAGILE-X SYNDROME - A HYPOTHESIS REGARDING THE MOLECULAR MECHANISM OF THE PHENOTYPE
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THYROID-FUNCTION IN MEN WITH FRAGILE X-LINKED MR
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AUTISM IS NOT ASSOCIATED WITH THE FRAGILE-X SYNDROME
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FRAGILE-X SYNDROME IN FEMALES WITH AUTISM
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FRAGILE-X FREQUENCY IN A MENTALLY-RETARDED POPULATION IN BRAZIL
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TRUE PRECOCIOUS PUBERTY IN A GIRL WITH THE FRAGILE X-SYNDROME
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FRAGILE-X FREQUENCY
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FRAGILE-X FREQUENCY - RESPONSE
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BIBLIOGRAPHY ON X-LINKED MENTAL-RETARDATION, THE FRAGILE-X, AND RELATED SUBJECTS .5. (1991)
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FRAGILE-X CHECKLIST
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DNA-BASED GENETIC TESTING IN 50 FRAGILE-X FAMILIES
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DNA LINKAGE ANALYSIS OF 26 FAMILIES WITH FRAGILE-X SYNDROME
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POSSIBLE ERASURE OF THE IMPRINT ON A FRAGILE-X CHROMOSOME WHEN TRANSMITTED BY A MALE
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COLLABORATIVE PROSPECTIVE-STUDY OF THE FRAGILE-X SYNDROME - REQUEST FOR PARTICIPATION
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TRANSFORMATION AND ESTABLISHMENT OF FRAGILE-X CELL-LINES FROM AMNIOCYTES
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NEW SOMATIC-CELL HYBRIDS FOR PHYSICAL MAPPING IN DISTAL XQ AND THE FRAGILE-X REGION
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FRAGILE-X EXPRESSION - USE OF A DOUBLE INDUCTION SYSTEM
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SV40-TRANSFORMED FRAGILE(X) AMNIOCYTES
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SHORT-TERM-MEMORY AND COGNITIVE VARIABILITY IN ADULT FRAGILE-X FEMALES
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SYNTACTIC DELAY AND PRAGMATIC DEVIANCE IN THE LANGUAGE OF FRAGILE-X MALES
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MENTAL IMPAIRMENT IN CYTOGENETICALLY POSITIVE FRAGILE-X FEMALES
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COGNITIVE PROFILES OF THE CARRIER FRAGILE-X WOMAN
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SEIZURE DISORDERS IN THE FRAGILE-X CHROMOSOME SYNDROME
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PITUITARY-GONADAL AXIS IN PREPUBERTAL BOYS WITH THE FRAGILE-X SYNDROME
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RISK CALCULATIONS IN THE FRAGILE-X SYNDROME
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RISK CALCULATIONS IN THE FRAGILE-X SYNDROME - REPLY
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ASSOCIATION OF THE ROBIN SEQUENCE WITH THE FRAGILE-X SYNDROME
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ANALYSIS OF NEOCORTEX IN 3 MALES WITH THE FRAGILE-X SYNDROME
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STUDY OF COLOR-VISION IN FRAGILE-X SYNDROME
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FREQUENCY OF THE COMMON FRAGILE SITE AT XQ27.2 UNDER CONDITIONS OF THYMIDYLATE STRESS - IMPLICATIONS FOR CYTOGENETIC DIAGNOSIS OF THE FRAGILE-X SYNDROME
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5TH INTERNATIONAL WORKSHOP ON THE FRAGILE-X AND X-LINKED MENTAL-RETARDATION
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