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Papers with one of the following phrases in the title:
fragile x or FMRP or trinucleotitde expansion or nucleotide expansion or cgg

Nodes: 2647, Authors: 5321, Journals: 428, Outer References: 16458, Words: 3536
Collection span: 1967 - 2005
View: Overview. Sorted by year, source, volume, issue, page.
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#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
120115211201 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):466-470
HOFSTEE Y; ARINAMI T; HAMAGUCHI H
COMPARISON BETWEEN THE CYTOGENETIC TEST FOR FRAGILE-X AND THE MOLECULAR ANALYSIS OF THE FMR-1 GENE IN JAPANESE MENTALLY-RETARDED INDIVIDUALS
1520
120211131202 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):471-473
HALLEY D; VANDENOUWELAND A; DEELEN W; VERMA I; OOSTRA B
STRATEGY FOR RELIABLE PRENATAL DETECTION OF NORMAL-MALE CARRIERS OF THE FRAGILE-X-SYNDROME
34
120327371203 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):474-481
HAGERMAN RJ; WILSON P; STALEY LW; LANG KA; FAN T; et al.
EVALUATION OF SCHOOL-CHILDREN AT HIGH-RISK FOR FRAGILE-X-SYNDROME UTILIZING BUCCAL CELL FMR-1 TESTING
1736
120416211204 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):482-485
VANDENOUWELAND AMW; DEVRIES BBA; BAKKER PLG; DEELEN WH; DEGRAAFF E; et al.
DNA DIAGNOSIS OF THE FRAGILE-X-SYNDROME IN A SERIES OF 236 MENTALLY-RETARDED SUBJECTS AND EVIDENCE FOR A REVERSAL OF MUTATION IN THE FMR-1 GENE
2935
12058101205 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):486-489
VONKOSKULL H; GAHMBERG N; SALONEN R; SALO A; PEIPPO M
FRAXA LOCUS IN FRAGILE-X DIAGNOSIS - FAMILY STUDIES, PRENATAL-DIAGNOSIS, AND DIAGNOSIS OF SPORADIC CASES OF MENTAL-RETARDATION
88
120617181206 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):490-496
MADDALENA A; HICKS BD; SPENCE WC; LEVINSON G; HOWARDPEEBLES PN
PRENATAL-DIAGNOSIS IN KNOWN FRAGILE-X CARRIERS
712
120712131207 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):497-500
SMITS A; SMEETS D; HAMEL B; DREESEN J; DEHAAN A; et al.
PREDICTION OF MENTAL STATUS IN CARRIERS OF THE FRAGILE-X MUTATION USING CGG REPEAT LENGTH
1316
120811131208 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):501-502
KAPLAN G; KUNG M; MCCLURE M; CRONISTER A
DIRECT MUTATION ANALYSIS OF 495 PATIENTS FOR FRAGILE-X CARRIER STATUS PROBAND DIAGNOSIS
46
120916171209 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):509-512
NOLIN SL; GLICKSMAN A; HOUCK GE; BROWN WT; DOBKIN CS
MOSAICISM IN FRAGILE-X AFFECTED MALES
3941
12109211210 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):513-516
DEELEN W; BAKKER C; HALLEY DJJ; OOSTRA BA
CONSERVATION OF CGG REGION IN FMR1 GENE IN MAMMALS
1116
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
121118331211 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):517-521
CHIURAZZI P; KOZAK L; NERI G
UNSTABLE TRIPLETS AND THEIR MUTATIONAL MECHANISM - SIZE-REDUCTION OF THE CGG REPEAT VS GERMLINE MOSAICISM IN THE FRAGILE-X-SYNDROME
915
12124111212 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):522-526
CHONG SS; EICHLER EE; NELSON DL; HUGHES MR
ROBUST AMPLIFICATION AND ETHIDIUM-VISIBLE DETECTION OF THE FRAGILE-X-SYNDROME CGG REPEAT USING PFU POLYMERASE
2542
121312211213 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):527-534
LEVINSON G; MADDALENA A; PALMER FT; HARTON GL; BICK DP; et al.
IMPROVED SIZING OF FRAGILE-X CCG REPEATS BY NESTED POLYMERASE CHAIN-REACTION
1829
1214001214 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):606-614
[Anon]
ABSTRACTS FOR THE 6TH INTERNATIONAL WORKSHOP ON FRAGILE-X-SYNDROME AND X-LINKED MENTAL-RETARDATION
00
121514171215 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 53(4):370-373
PUISSANT H; MALINGE MC; LARGETPIET A; MARTIN D; CHAUVEAU P; et al.
MOLECULAR ANALYSIS OF 53 FRAGILE-X FAMILIES WITH THE PROBE-STB12.3
12
1216121216 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 53(4):380-381
PARK V; HOWARDPEEBLES P; SHERMAN S; TAYLOR A; WULFSBERG E
POLICY STATEMENT - AMERICAN-COLLEGE-OF-MEDICAL-GENETICS - FRAGILE-X-SYNDROME - DIAGNOSTIC AND CARRIER TESTING
1728
1217031217 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 53(4):382-382
HOWARDPEEBLES PN; MADDALENA A; SPENCE WC; LEVINSON G; FALLON L; et al.
FRAGILE-X SCREENING - WHAT IS THE REAL ISSUE
59
12189281218 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 54(2):141-143
CRADDOCK N; DANIELS J; MCGUFFIN P; OWEN M
VARIATION AT THE FRAGILE X-LOCUS DOES NOT INFLUENCE SUSCEPTIBILITY TO BIPOLAR DISORDER
16
121913281219 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 54(4):378-383
THOMPSON NM; GULLEY ML; ROGENESS GA; CLAYTON RJ; JOHNSON C; et al.
NEUROBEHAVIORAL CHARACTERISTICS OF CGG AMPLIFICATION STATUS IN FRAGILE-X FEMALES
2028
122016331220 1994 AMERICAN JOURNAL ON MENTAL RETARDATION 98(4):455-462
KERBY DS; DAWSON BL
AUTISTIC FEATURES, PERSONALITY, AND ADAPTIVE-BEHAVIOR IN MALES WITH THE FRAGILE-X SYNDROME AND NO AUTISM
1423
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
122119411221 1994 AMERICAN JOURNAL ON MENTAL RETARDATION 98(5):567-579
LACHIEWICZ AM; SPIRIDIGLIOZZI GA; GULLION CM; RANSFORD SN; RAO K
ABERRANT BEHAVIORS OF YOUNG BOYS WITH FRAGILE X-SYNDROME
2833
1222001222 1994 ANNALS OF NEUROLOGY 36(3):544-544
GUERREIRO M; MOURARIBEIRO MV; KATO M; CAMARGO E; DEFARIA APM
BRAIN SINGLE-PHOTON EMISSION COMPUTED-TOMOGRAPHY IMAGING IN FRAGILE-X SYNDROME
00
122310111223 1994 ARCHIVES OF PEDIATRICS & ADOLESCENT MEDICINE 148(1):63-64
LEUNG AKC; MCLEOD DR; ROBSON WLM; FAGAN JE
PICTURE OF THE MONTH - FRAGILE-X SYNDROME
01
122414281224 1994 BRITISH JOURNAL OF CLINICAL PRACTICE 48(1):42-44
PATEL BD
THE FRAGILE-X SYNDROME
11
1225001225 1994 CANADIAN FAMILY PHYSICIAN 40:290-295
WIEBE E; WIEBE A
FRAGILE-X SYNDROME
01
12261161226 1994 CANCER RESEARCH 54(19):5212-5216
LEE ST; MCGLENNEN RC; LITZ CE
CLONAL DETERMINATION BY THE FRAGILE-X (FMR1) AND PHOSPHOGLYCERATE KINASE (PGK) GENES IN HEMATOLOGICAL MALIGNANCIES
112
122716391227 1994 CELL 77(1):33-39
SIOMI H; CHOI MY; SIOMI MC; NUSSBAUM RL; DREYFUSS G
ESSENTIAL ROLE FOR KH DOMAINS IN RNA-BINDING - IMPAIRED RNA-BINDING BY A MUTATION IN THE KH DOMAIN OF FMR1 THAT CAUSES FRAGILE-X SYNDROME
74266
122821531228 1994 CELL 77(6):853-861
KUNST CB; WARREN ST
CRYPTIC AND POLAR VARIATION OF THE FRAGILE-X REPEAT COULD RESULT IN PREDISPOSING NORMAL ALLELES
101244
122923521229 1994 CELL 78(1):23-33
BAKKER CE; VERHEIJ C; WILLEMSEN R; VANDERHELM R; OERLEMANS F; et al.
FMR1 KNOCKOUT MICE - A MODEL TO STUDY FRAGILE-X MENTAL-RETARDATION
96163
123010231230 1994 CLINICAL GENETICS 45(4):175-180
SCHRANDERSTUMPEL C; GERVER WJ; MEYER H; ENGELEN J; MULDER H; et al.
PRADER-WILLI-LIKE PHENOTYPE IN FRAGILE-X SYNDROME
417
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
1231671231 1994 CLINICAL GENETICS 45(4):186-189
LOPEZPAJARES I; DELICADO A; PASCUALCASTROVIEJO I; LOPEZMARTIN V; MORENO F; et al.
FRAGILE-X SYNDROME WITH EXTRA MICROCHROMOSOME
01
123219641232 1994 DEVELOPMENTAL BRAIN DYSFUNCTION 7(2-3):155-164
HAGERMAN RJ; FULTON MJ; LEAMAN A; RIDDLE J; HAGERMAN K; et al.
A SURVEY OF FLUOXETINE THERAPY IN FRAGILE-X SYNDROME
1719
123358911233 1994 EUROPEAN JOURNAL OF CLINICAL INVESTIGATION 24(1):1-10
ROUSSEAU F
THE FRAGILE-X SYNDROME - IMPLICATIONS OF MOLECULAR-GENETICS FOR THE CLINICAL SYNDROME
811
12340191234 1994 GENES CHROMOSOMES & CANCER 9(2):141-144
RIGGINS GJ; SHERMAN SL; PHILLIPS CN; STOCK W; WESTBROOK CA; et al.
CGG-REPEAT POLYMORPHISM OF THE BCR GENE RULES OUT PREDISPOSING ALLELES LEADING TO THE PHILADELPHIA-CHROMOSOME
18
12355301235 1994 GENETIC COUNSELING 5(2):129-139
MAES B; FRYNS JP; VANWALLEGHEM M; VANDENBERGHE H
PERSONAL INDEPENDENCE OF ADULT MENTALLY-RETARDED MEN WITH FRAGILE-X SYNDROME
00
1236461236 1994 GENETIC COUNSELING 5(4):377-380
WIEGERS AM; CURFS LMG; MEIJER H; OOSTRA B; FRYNS JP
A DELETION OF 1.6 KB PROXIMAL TO THE CGG REPEAT OF THE FMR1-GENE CAUSES FRAGILE X-LIKE PSYCHOLOGICAL FEATURES
00
123719281237 1994 HUMAN GENETICS 93(2):143-147
VAISANEN ML; KAHKONEN M; LEISTI J
DIAGNOSIS OF FRAGILE-X SYNDROME BY DIRECT MUTATION ANALYSIS
1012
123821341238 1994 HUMAN GENETICS 94(4):395-400
MILA M; KRUYER H; GLOVER G; SANCHEZ A; CARBONELL P; et al.
MOLECULAR ANALYSIS OF THE (CGG)(N) EXPANSION IN THE FMR-1 GENE IN 59 SPANISH FRAGILE-X SYNDROME FAMILIES
1516
123913191239 1994 HUMAN GENETICS 94(5):479-483
HAATAJA R; VAISANEN ML; LI MY; RYYNANEN M; LEISTI J
THE FRAGILE-X SYNDROME IN FINLAND - DEMONSTRATION OF A FOUNDER EFFECT BY ANALYSIS OF MICROSATELLITE HAPLOTYPES
1520
124018251240 1994 HUMAN GENETICS 94(5):523-526
VITS L; DEBOULLE K; REYNIERS E; HANDIG I; DARBY JK; et al.
APPARENT REGRESSION OF THE CGG REPEAT IN FMR1 TO AN ALLELE OF NORMAL SIZE
1620
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
124123311241 1994 HUMAN MOLECULAR GENETICS 3(3):393-398
REISS AL; KAZAZIAN HH; KREBS CM; MCAUGHAN A; BOEHM CD; et al.
FREQUENCY AND STABILITY OF THE FRAGILE-X PREMUTATION
3461
124220281242 1994 HUMAN MOLECULAR GENETICS 3(3):399-405
MACPHERSON JN; BULLMAN H; YOUINGS SA; JACOBS PA
INSERT SIZE AND FLANKING HAPLOTYPE IN FRAGILE-X AND NORMAL-POPULATIONS - POSSIBLE MULTIPLE ORIGINS FOR THE FRAGILE-X MUTATION
3758
1243131243 1994 HUMAN MOLECULAR GENETICS 3(3):521-521
JOKINEN E; SAKAI J; YAMAMOTO T; HOBBS HH
CGG TRIPLE REPEAT POLYMORPHISM IN VLDL RECEPTOR (VLDL-R) GENE
016
124421331244 1994 HUMAN MOLECULAR GENETICS 3(4):615-620
MEIJER H; DEGRAAFF E; MERCKX DML; JONGBLOED RJE; DEDIESMULDERS CEM; et al.
A DELETION OF 1.6 KB PROXIMAL TO THE CGG REPEAT OF THE FMR1 GENE CAUSES THE CLINICAL PHENOTYPE OF THE FRAGILE X SYNDROME
5078
124518291245 1994 HUMAN MOLECULAR GENETICS 3(9):1543-1551
SNOW K; TESTER DJ; KRUCKEBERG KE; SCHAID DJ; THIBODEAU SN
SEQUENCE-ANALYSIS OF THE FRAGILE-X TRINUCLEOTIDE REPEAT - IMPLICATIONS FOR THE ORIGIN OF THE FRAGILE-X MUTATION
64115
124627461246 1994 HUMAN MOLECULAR GENETICS 3(9):1553-1560
HIRST MC; GREWAL PK; DAVIES KE
PRECURSOR ARRAYS FOR TRIPLET REPEAT EXPANSION AT THE FRAGILE-X LOCUS
56108
12477181247 1994 INTELLIGENCE 19(1):45-50
DANIELS JK; OWEN MJ; MCGUFFIN P; THOMPSON L; DETTERMAN DK; et al.
IQ AND VARIATION IN THE NUMBER OF FRAGILE-X CGG REPEATS - NO ASSOCIATION IN A NORMAL SAMPLE
29
1248151248 1994 ITALIAN JOURNAL OF NEUROLOGICAL SCIENCES 15(7):365-368
MUSUMECI SA; ELIA M; FERRI R; SCUDERI C; DELGRACCO S
EVOKED SPIKES AND GIANT SOMATOSENSORY-EVOKED POTENTIALS IN A PATIENT WITH FRAGILE-X SYNDROME
38
1249111249 1994 JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION 271(1):28-28
BROWN WT; HOUCK GE; JEZIOROWSKA A; LEVINSON FN; DING X; et al.
RAPID FRAGILE-X CARRIER SCREENING AND PRENATAL-DIAGNOSIS USING A NONRADIOACTIVE PCR TEST (VOL 270, PG 1569, 1993)
11
125030481250 1994 JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION 271(7):507-514
TAYLOR AK; SAFANDA JF; FALL MZ; QUINCE C; LANG KA; et al.
MOLECULAR PREDICTORS OF COGNITIVE INVOLVEMENT IN FEMALE CARRIERS OF FRAGILE-X SYNDROME
8092
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
125142811251 1994 JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION 271(7):536-542
WARREN ST; NELSON DL
ADVANCES IN MOLECULAR ANALYSIS OF FRAGILE-X SYNDROME
74129
125213161252 1994 JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION 271(7):552-553
CASKEY CT
FRAGILE-X SYNDROME - IMPROVING UNDERSTANDING AND DIAGNOSIS
22
125320241253 1994 JAPANESE JOURNAL OF GENETICS 69(3):259-267
SEKI N; ISHIKIRIYAMA S; YAMAUCHI M; HORI T
CYTOGENETIC AND MOLECULAR ANALYSIS OF DYNAMIC MUTATION ASSOCIATED WITH FRAGILE-X SYNDROME
00
125410231254 1994 JOURNAL OF AUTISM AND DEVELOPMENTAL DISORDERS 24(4):473-485
MAZZOCCO MMM; PENNINGTON BF; HAGERMAN RJ
SOCIAL COGNITION SKILLS AMONG FEMALES WITH FRAGILE-X
912
1255001255 1994 JOURNAL OF CELLULAR BIOCHEMISTRY :184-184
WARREN ST
OVERVIEW AND UPDATE ON FMR1 AND FRAGILE-X SYNDROME
00
12569201256 1994 JOURNAL OF INTELLECTUAL DISABILITY RESEARCH 38:1-8
DEVRIES LBA; HALLEY DJJ; OOSTRA BA; NIERMEIJER MF
THE FRAGILE-X SYNDROME - A GROWING GENE CAUSING FAMILIAL INTELLECTUAL DISABILITY
12
125716271257 1994 JOURNAL OF INTELLECTUAL DISABILITY RESEARCH 38:27-35
SABARATNAM M; LAVER S; BUTLER L; PEMBREY M
FRAGILE-X SYNDROME IN NORTH-EAST ESSEX - TOWARDS SYSTEMATIC SCREENING - CLINICAL-SELECTION
68
1258381258 1994 JOURNAL OF MEDICAL GENETICS 31(1):76-78
TEJADA MI; MORNET E; TIZZANO E; MOLINA M; BAIGET M; et al.
IDENTIFICATION BY MOLECULAR DIAGNOSIS OF MOSAIC TURNERS-SYNDROME IN AN OBLIGATE CARRIER FEMALE FOR FRAGILE-X SYNDROME
48
1259001259 1994 JOURNAL OF MEDICAL GENETICS 31(2):170-170
STRAIN L; PORTEOUS MEM; BONTHRON DT
PRENATAL-DIAGNOSIS OF FRAGILE-X SYNDROME - MANAGEMENT OF THE MALE FETUS WITH A PREMUTATION
00
1260001260 1994 JOURNAL OF MEDICAL GENETICS 31(2):173-173
WANG Q; GREEN EP; MATHEW CG; BOBROW M
NONRADIOACTIVE PCR BASED SCREENING FOR FRAGILE-X SYNDROME
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
1261001261 1994 JOURNAL OF MEDICAL GENETICS 31(2):173-173
BULLOCK S; LINDLEY V
COMPLEMENTARY CYTOGENETIC AND MOLECULAR ANALYSIS OF A REFERRAL FOR FRAGILE-X TESTING
00
1262131262 1994 JOURNAL OF MEDICAL GENETICS 31(3):260-261
GILLESSENKAESBACH G; HORSTHEMKE B
CLINICAL AND MOLECULAR STUDIES IN FRAGILE-X PATIENTS WITH A PRADER-WILLI-LIKE PHENOTYPE
03
1263121263 1994 JOURNAL OF MEDICAL GENETICS 31(10):820-820
DEVRIES BBA; NIERMEIJER MF
THE PRADER-WILLI-LIKE PHENOTYPE IN FRAGILE-X PATIENTS - A DESIGNATION FACILITATING CLINICAL (AND MOLECULAR) DIFFERENTIAL-DIAGNOSIS
16
12646121264 1994 JOURNAL OF MEDICAL GENETICS 31(12):950-952
CURTIS G; DENNIS N; MACPHERSON J
THE IMPACT OF GENETIC-COUNSELING ON FEMALES IN FRAGILE-X FAMILIES
11
12652441265 1994 JOURNAL OF MOLECULAR BIOLOGY 243(2):143-151
SMITH SS; LAAYOUN A; LINGEMAN RG; BAKER DJ; RILEY J
HYPERMETHYLATION OF TELOMERE-LIKE FOLDBACKS AT CODON-12 OF THE HUMAN C-HA-RAS GENE AND THE TRINUCLEOTIDE REPEAT OF THE FMR-1 GENE OF FRAGILE-X
1255
126618331266 1994 JOURNAL OF THE AMERICAN ACADEMY OF CHILD AND ADOLESCENT PSYCHIATRY 33(2):247-255
SOBESKY WE; HULL CE; HAGERMAN RJ
SYMPTOMS OF SCHIZOTYPAL PERSONALITY-DISORDER IN FRAGILE-X WOMEN
2136
126711371267 1994 JOURNAL OF THE AMERICAN ACADEMY OF CHILD AND ADOLESCENT PSYCHIATRY 33(2):256-264
DORN MB; MAZZOCCO MMM; HAGERMAN RJ
BEHAVIORAL AND PSYCHIATRIC-DISORDERS IN ADULT MALE CARRIERS OF FRAGILE-X
2533
126815181268 1994 JOURNAL OF THE AMERICAN ACADEMY OF CHILD AND ADOLESCENT PSYCHIATRY 33(9):1316-1321
MERENSTEIN SA; SHYU V; SOBESKY WE; STALEY L; BERRYKRAVIS E; et al.
FRAGILE-X SYNDROME IN A NORMAL IQ MALE WITH LEARNING AND EMOTIONAL-PROBLEMS
1822
1269161269 1994 KLINISCHE PADIATRIE 206(5):410-411
FEHLOW P; MIOSGE W; WALTHER F
ASSOCIATION OF SAETHRE-CHOTZEN-SYNDROME AND FRAGILE-X-SYNDROME
00
1270251270 1994 LANCET 344(8935):1500-1500
TURNER G; ROBINSON H; WAKE S; MARTIN N
DIZYGOUS TWINNING AND PREMATURE MENOPAUSE IN FRAGILE-X SYNDROME
3352
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
1271221271 1994 MENTAL RETARDATION 32(2):156-156
SPITZ HH
FRAGILE-X SYNDROME IS NOT THE 2ND LEADING CAUSE OF MENTAL-RETARDATION
01
1272481272 1994 MOLECULAR AND CELLULAR PROBES 8(2):177-180
CAO J; TARLETON J; BARBERIO D; DAVIDOW LS
A SIMPLE FRAGILE-X PCR ASSAY WITH 7-DEAZAGUANINE-SUBSTITUTED DNA VISUALIZED BY ETHIDIUM-BROMIDE
25
12738101273 1994 MOLECULAR AND CELLULAR PROBES 8(3):241-244
DAVIDOW LS; BARBERIO D; CAO J; MCCORMICK I
AN IMPROVED FRAGILE-X SOUTHERN BLOT PROBE WITHOUT THE CGGS ELIMINATES BACKGROUND BANDS
00
127423411274 1994 NATURE GENETICS 8(1):88-94
EICHLER EE; HOLDEN JJA; POPOVICH BW; REISS AL; SNOW K; et al.
LENGTH OF UNINTERRUPTED CGG REPEATS DETERMINES INSTABILITY IN THE FMR1 GENE
92243
1275001275 1994 NEUROLOGY 44(4):A400-A400
GUERREIRO M; MOURARIBEIRO MVL; CAMARGO EE; KATO M; MENEZES JR; et al.
NEUROBIOLOGY OF FRAGILE-X-SYNDROME (FXS)
00
127622611276 1994 NEUROLOGY 44(7):1317-1324
REISS AL; LEE J; FREUND L
NEUROANATOMY OF FRAGILE-X SYNDROME - THE TEMPORAL-LOBE
5489
12777411277 1994 NEUROPHYSIOLOGIE CLINIQUE-CLINICAL NEUROPHYSIOLOGY 24(6):413-426
FERRI R; MUSUMECI SA; ELIA M; DELGRACCO S; SCUDERI C; et al.
BIT-MAPPED SOMATOSENSORY-EVOKED POTENTIALS IN THE FRAGILE-X SYNDROME
715
12783261278 1994 NUCLEIC ACIDS RESEARCH 22(9):1735-1740
HAN J; HSU CC; ZHU Z; LONGSHORE JW; FINLEY WH
OVER-REPRESENTATION OF THE DISEASE-ASSOCIATED (CAG) AND (CGG) REPEATS IN THE HUMAN GENOME
225
1279001279 1994 PEDIATRIC RESEARCH 35(4):A23-A23
LACHIEWICZ AM; DAWSON DV
AUTISTIC BEHAVIORS OF YOUNG GIRLS WITH FRAGILE X-SYNDROME
11
128014311280 1994 PEDIATRICS 93(6):992-995
LACHIEWICZ AM; DAWSON DV
DO YOUNG BOYS WITH FRAGILE-X-SYNDROME HAVE MACROORCHIDISM
1317
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
128116211281 1994 PRENATAL DIAGNOSIS 14(6):469-474
STRAIN L; PORTEOUS MEM; GOSDEN CM; ELLIS PM; NEILSON JP; et al.
PRENATAL-DIAGNOSIS OF FRAGILE-X-SYNDROME - MANAGEMENT OF THE MALE FETUS WITH A PREMUTATION
34
128210301282 1994 PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA 91(11):4950-4954
FRY M; LOEB LA
THE FRAGILE-X SYNDROME D(CGG)(N) NUCLEOTIDE REPEATS FORM A STABLE TETRAHELICAL STRUCTURE
39148
12832111283 1994 THERIOGENOLOGY 42(5):789-794
LLAMBI S; POSTIGLIONI A
LOCALIZATION OF THE FRAGILE-X CHROMOSOME BREAK POINTS IN HOLSTEIN-FRIESIAN CATTLE (BOS-TAURUS)
02
1284001284 1995 AMERICAN JOURNAL OF EPIDEMIOLOGY 141(11):S50-S50
DAWSON DV; LACHIEWICZ AM
BEHAVIORAL EPIDEMIOLOGY OF FRAGILE-X SYNDROME IN FEMALE PEDIATRIC POPULATIONS
00
128520371285 1995 AMERICAN JOURNAL OF HUMAN GENETICS 56(5):1042-1051
QUAN F; ZONANA J; GUNTER K; PETERSON KL; MAGENIS RE; et al.
AN ATYPICAL CASE OF FRAGILE-X SYNDROME CAUSED BY A DELETION THAT INCLUDES THE FMRI GENE
1930
128619651286 1995 AMERICAN JOURNAL OF HUMAN GENETICS 56(5):1147-1155
FISCH GS; SNOW K; THIBODEAU SN; CHALIFAUX M; HOLDEN JJA; et al.
THE FRAGILE-X PREMUTATION IN CARRIERS AND ITS EFFECT ON MUTATION SIZE IN OFFSPRING
2835
128721511287 1995 AMERICAN JOURNAL OF HUMAN GENETICS 57(2):351-361
ZHONG N; YANG WH; DOBKIN C; BROWN WT
FRAGILE-X GENE INSTABILITY - ANCHORING AGGS AND LINKED MICROSATELLITES
5482
128836541288 1995 AMERICAN JOURNAL OF HUMAN GENETICS 57(3):609-618
DEGRAAFF E; WILLEMSEN R; ZHONG N; DEDIESMULDERS CEM; BROWN WT; et al.
INSTABILITY OF THE CGG REPEAT AND EXPRESSION OF THE FMR1 PROTEIN IN A MALE FRAGILE-X PATIENT WITH A LUNG-TUMOR
2632
1289001289 1995 AMERICAN JOURNAL OF HUMAN GENETICS 57(4):40-40
FENG Y; EBERHART DE; WARREN ST
THE PROTEIN ABSENT IN FRAGILE-X SYNDROME (FMRP) IS A RIBOSOME-ASSOCIATED PROTEIN
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EXPANDING THE ROLE OF THE GENETIC COUNSELOR WORKING WITH FRAGILE-X FAMILIES
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SINGLE-CELL DETECTION OF THE FMR1, HD, AND SCA1 TRINUCLEOTIDE REPEATS - APPLICATION TO PREIMPLANTATION DIAGNOSIS AND INSTABILITY ANALYSIS OF FRAGILE-X SYNDROME, HUNTINGTON DISEASE, AND SPINO-CEREBELLAR ATAXIA TYPE-1
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PREIMPLANTATION GENETIC TESTING (PGT) FOR FRAGILE-X (FRAX)
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IDENTIFICATION OF A CYTOPLASMIC ANCHOR DOMAIN RESPONSIBLE FOR THE SUBCELLULAR-LOCALIZATION OF THE FRAGILE-X MENTAL-RETARDATION PROTEIN, FMRP
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EVOLUTION OF THE CRYPTIC FMR1 CGG REPEAT
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CLINICAL-CRITERIA FOR FRAGILE-X SOUTHERN BLOT DNA DIAGNOSTIC TESTING
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A CONTROLLED-STUDY OF LONGITUDINAL IQ CHANGES IN FEMALES AND MALES WITH FRAGILE-X SYNDROME
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THRESHOLD CGG REPEAT SIZE FOR FRAGILE SITE EXPRESSION WITHOUT METHYLATION IDENTIFIED IN LYMPHOCYTE, LYMPHOBLASTOID AND CLONAL LYMPHOBLASTOID CULTURES FROM AN FMR1 UNMETHYLATED MOSAIC FULL MUTATION INDIVIDUAL
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A 5-YEAR EXPERIENCE WITH FRAGILE-X TESTING
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SELECTION AGAINST A MARKER CHROMOSOME IN FRAGILE-X-STRESSED CULTURES
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VARIATIONS IN THE LENGTH OF THE CGG-REPEAT OF FMR-1 AFFECT GENE-EXPRESSION
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ASHLEY AE; MEADOWS KL; SHERMAN SL
TRANSMISSION CHARACTERISTICS OF THE FMR-1 MUTATION IN THE COLLABORATIVE PROSPECTIVE-STUDY OF THE FRAGILE-X SYNDROME
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FRAGILE-X FOUNDER CHROMOSOME EFFECTS AND NEW MUTATIONS
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FRAGILE-X SYNDROME - ROUNDER CHROMOSOMES IN ITALY
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EVIDENCE FOR A FAMILIAL FACTOR INVOLVED IN CGG REPEAT EXPANSION IN FRAGILE-X SYNDROME
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NEW INTRAGENIC ALU POLYMORPHISMS IN THE FRAGILE-X GENE
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LONG UNINTERRUPTED CGG REPEATS WITHIN THE FMR1 GENE - POSSIBLE MECHANISM FOR THE PREVALENCE OF THE FRAGILE-X SYNDROME AMONG TUNISIAN JEWS
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MUTATIONS IN THE CPG ISLAND OF THE FMR1 GENE - ARE THEY RESPONSIBLE FOR FRAGILE-X SYNDROME
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PULKKINEN L; MANNERMAA A; KAJANOJA E; RYYNANANEN M; SAARIKOSKI S
DELETION IN THE FMR1 GENE IN A FRAGILE-X-MALE
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RAPID SCREENING-TEST FOR FRAGILE-X SYNDROME
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INSTABILITY OF THE CGG REPEAT AND EXPRESSION OF FMR1 PROTEIN IN A MALE-PATIENT WITH A LUNG-TUMOR
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HART PS; OLSON SM; CRANDALL K; TARLETON J
FRAGILE-X SYNDROME RESULTING FROM A 400 BASEPAIR DELETION WITHIN THE FMR1 GENE
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TRANSMISSION OF STABLE AND UNSTABLE PREMUTATIONS FROM GREAT-GRANDMOTHER AND GREAT-GRANDFATHER RESPECTIVELY - LESSONS FOR GENETIC-COUNSELING IN FRAGILE-X SYNDROME FAMILIES
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BUCHANAN JA; KLOCK RJ; DORAN K; KENNEDY D; WYATT P
PRENATAL TEST FOR FRAGILE-X SYNDROME REVEALS APPARENT FMR1 GENE CONTRACTION
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SHAPIRO LR; WILMOT PL; MARINELLO MJ
NONINDUCED FRAGILE-X CHROMOSOMES DETECTED IN ROUTINE AMNIOTIC-FLUID CELL-CULTURE - DETERMINATION OF SIGNIFICANCE
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ACCEPTANCE OF SCREENING FOR THE FRAGILE-X SYNDROME AMONG 1878 MENTALLY-RETARDED INDIVIDUALS IN INSTITUTES AND SPECIAL SCHOOLS IN THE NETHERLANDS
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FRAGILE-X PREMUTATION FREQUENCY IN NORTHERN THAILAND
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A SINGLE TUBE NONRADIOACTIVE PCR ASSAY FOR THE DETECTION OF THE FULL SPECTRUM OR FMR1 CGG REPEATS SEEN IN THE NORMAL, CARRIER AND FRAGILE-X SYNDROME INDIVIDUALS
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JOHNSON DB; QUAN F; BUCHANNAN JA; POPOVICH BW
ALLELIC SIZE LADDERS FCR THE ACCURATE SIZING OF TRINUCLEOTIDE REPEATS IN HUNTINGTON DISEASE AND FRAGILE-X SYNDROME
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IDENTIFICATION OF THE NUMBER OF THE FRAGILE-X SYNDROME CGG REPEAT USING SILVER STAIN
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BROWN CA; BRASINGTON CK; GRASS FS
PATERNAL TRANSMISSION OF A FULL MUTATION IN THE FMR1 GENE - IDENTIFICATION OF PATERNAL CGG REPEAT SHES IN MULTIPLE TISSUES
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THE HIGH PREVALENCE OF FRAGILE-X PREMUTATION CARRIER FEMALES - IS THIS FREQUENCY UNIQUE TO THE FRENCH-CANADIAN POPULATION
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PREVALENCE OF CARRIERS OF PREMUTATION-SIZE ALLELES OF THE FMRI GENE AND IMPLICATIONS FOR THE POPULATION-GENETICS OF THE FRAGILE-X SYNDROME
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EXPANSION OF THE CGG REPEAT IN FRAGILE-X IN THE FMR1 GENE DEPENDS ON THE SEX OF THE OFFSPRING
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POPULATION-DYNAMICS OF A MEIOTIC MITOTIC EXPANSION MODEL FOR THE FRAGILE-X SYNDROME
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GERMLINE MOSAICISM AT THE FRAGILE-X LOCUS
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FRAGILE-X SCREENING - WHAT IS THE REAL ISSUE
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GROWTH IN STATURE IN FRAGILE-X FAMILIES - A MIXED LONGITUDINAL-STUDY
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DISSEMINATION OF GENETIC RISK INFORMATION TO RELATIVES IN THE FRAGILE-X SYNDROME - GUIDELINES FOR GENETIC COUNSELORS
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LACK OF SIGNIFICANT ASSOCIATION BETWEEN SPINA-BIFIDA AND THE FRAGILE-X SYNDROME
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WORD-FINDING DIFFICULTIES, VERBAL PARAPHASIAS, AND VERBAL DYSPRAXIA IN 10 INDIVIDUALS WITH FRAGILE-X-SYNDROME
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FRAGILE-X SYNDROME - DISCORDANT LEVELS OF CGG REPEAT MOSAICISM IN 2 BROTHERS
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Adult fragile X syndrome: Neuropsychology, brain anatomy, and metabolism
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CARRIER DIAGNOSIS OF THE FRAGILE-X SYNDROME - A CHALLENGE IN ANTENATAL CLINICS
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OVEREXPRESSION OF FRAGILE-X GENE (FMR-1) TRANSCRIPTS IN NEURAL CELLS RESULTS IN INCREASED LEVELS OF CYCLIC ADENOSINE-MONOPHOSPHATE PRODUCTION
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TRIPLET REPEAT EXPANSION MUTATIONS - THE EXAMPLE OF FRAGILE-X SYNDROME
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FRAGILE-X SYNDROME
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DNA TESTING FOR FRAGILE-X SYNDROME IN SCHOOLS FOR LEARNING-DIFFICULTIES
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TREATMENT OF FRAGILE-X SYNDROME
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Molecular characterization of the fragile-X syndrome in the Mexican population
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Rat PPAR delta contains a CGG triplet repeat and is prominently expressed in the thalamic nuclei
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THE TRINUCLEOTIDE REPEAT SEQUENCE D(CGG)(15) FORMS A HEAT-STABLE HAIRPIN CONTAINING G(SYN)CENTER-DOT-G(ANTI) BASE-PAIRS
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THE FRAGILE-X SYNDROME
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FRAGILE-X SYNDROME
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CRYSTAL-STRUCTURE OF THE A-DNA DECAMER D(CCIGGCCM(5)CGG) AT 1.6-ANGSTROM SHOWING THE UNEXPECTED WOBBLE I-CENTER-DOT-M(5)C BASE-PAIR
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DETERMINATION OF THE HYDROGEN-BONDED STRUCTURE OF CGG TRIMERS IN CHLOROFORM SOLUTION BY VIBRATIONAL SPECTROSCOPY
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ALLOGENEIC BMT FROM A DONOR WITH FRAGILE-X SYNDROME - CYTOGENETIC AND MOLECULAR EVALUATION
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NONRADIOACTIVE DNA DIAGNOSIS FOR THE FRAGILE-X SYNDROME IN MENTALLY-RETARDED JAPANESE MALES
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THE INCIDENCE OF THE FRAGILE-X SYNDROME IN JAPANESE - COMMENTARY ON NANBAS PAPER
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NONRADIOACTIVE DNA DIAGNOSIS FOR THE FRAGILE-X SYNDROME IN JAPANESE MENTALLY-RETARDED MALES - COMMENT
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VARIABLE EXPRESSION OF DEVELOPMENTAL GERSTMANN SIGNS IN FRAGILE-X SYNDROME
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DISSOCIATIONS IN DEVELOPMENTAL DYSCALCULIA SECONDARY TO FRAGILE-X SYNDROME
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BEHAVIOR AND DEVELOPMENT IN FRAGILE-X SYNDROME - DYKENS,E
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STUDY SUPPORTS SCREENING FOR THE FRAGILE-X-SYNDROME
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RAPID, NONRADIOACTIVE SOUTHERN BLOT METHOD FOR DETECTING FRAGILE-X MUTATIONS
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Perspectives and molecular diagnosis of the fragile X syndrome
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IT IS TIME TO ABANDON THE CYTOGENETIC FRAGILE-X TEST
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Conference summary: Fourth International Conference on Fragile X and X-linked Mental Retardation sponsored by the National Fragile X Foundation
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Report of the Executive Director of the National Fragile X Foundation
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Quantitative brain imaging studies of fragile X syndrome
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Fragile X and the amygdala: Cognitive, interpersonal, emotional, and neuroendocrine considerations
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Sleep neurophysiology in fragile X patients
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Ocular findings in fragile X syndrome
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Longitudinal IQ changes in fragile X females
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Preliminary report on cognitive and adaptive behaviors of preschool-aged males with fragile X
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Behavioral profiles of autistic and nonautistic fragile X males
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Arousal difficulties in males with fragile X syndrome: A preliminary report
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Dimensions of shyness in fragile X females
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An update on fragile X prenatal diagnosis: End of the cytogenetic testing era
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Distribution and frequency of FMR1 CGG repeat number in institutionalized developmentally disabled individuals
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Assessment of counselling of normal males and normal transmitting male carriers identified in fragile X families
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Fragile X syndrome: What is the impact of diagnosis on families?
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Survey of the efficacy of clonidine in fragile X syndrome
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Protein therapy in fragile X syndrome - A brief overview of principles, potentials and problems
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Introduction to fragile X syndrome for parents
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Females with fragile X: A parent's perspective
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Workshop for family and friends .1. The fragile X gene and its mutations
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Educating extended family members about the inheritance of the fragile X syndrome
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Psychological and emotional studies of the fragile X mutation - A workshop summary
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Distribution and frequency of FMR1 CGG repeat numbers in the general population
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Fragile X screening in pediatric and obstetrical patients
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4th International Fragile X and X-Linked Mental Retardation Conference - Albuquerque, NM, USA, June 8-12, 1994 - Abstracts
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MOLECULAR DIAGNOSIS OF FRAGILE-X SYNDROME
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FXR1, AN AUTOSOMAL HOMOLOG OF THE FRAGILE-X MENTAL-RETARDATION GENE
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THE FRAGILE-X MENTAL-RETARDATION SYNDROME PROTEIN INTERACTS WITH NOVEL HOMOLOGS FXR1 AND FXR2
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KLUGER G; BOHM I; LAUB MC; WALDENMEIER C; STUHRMANNSPANGENBERG M
EEG IN CHILDREN WITH FRAGILE-X PREMUTATION
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SINGH R; SUTHERLAND G; MANSON J
SEIZURES WITH EPILEPTOGENIC EEG PATTERN IN 2 SISTERS WITH FRAGILE X-SYNDROME
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Confirmation of early menopause in fragile X carriers
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1491221491 1996 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):376-376
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Normal age of menarche in fragile X syndrome
33
1492461492 1996 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):377-377
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Successful pregnancy in a fragile X carrier by donor egg
23
1493071493 1996 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):378-381
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Experiences and attitudes concerning genetic testing and insurance in a Colorado population: A survey of families diagnosed with fragile X syndrome
09
14943181494 1996 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):395-398
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Fragile X mutation and FG syndrome-like phenotype
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Segregation of the fragile X mutation from a male with a full mutation: Unusual somatic instability in the FMR-1 locus
13
149612201496 1996 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):413-414
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Fragile X: Clinical associations
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00

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