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Tue Aug 24 10:43:57 2004
All papers with "Fragile X" in the title.

Nodes: 2369
Authors: 4634, Journals: 373, Outer References: 14152
Collection span: 1980 - 2004
View: Overview. Sorted by NCR.
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#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
40113391910 2000 JOURNAL OF DEVELOPMENTAL AND BEHAVIORAL PEDIATRICS 21(4):278-282
Wisbeck JM; Huffman LC; Freund L; Gunnar MR; Davis EP; Reiss AL
Cortisol and social stressors in children with fragile X: A pilot study
810
40227391988 2001 AMERICAN JOURNAL OF MEDICAL GENETICS 103(4):314-319
Johnston C; Eliez S; Dyer-Friedman J; Hessl D; Glaser B; Blasey C; Taylor A; Reiss A
Neurobehavioral phenotype in carriers of the fragile X premutation
55
40317392147 2002 JOURNAL OF AUTISM AND DEVELOPMENTAL DISORDERS 32(2):107-114
Fisch GS; Simensen RJ; Schroer RJ
Longitudinal changes in cognitive and adaptive Behavior scores in children and adolescents with the fragile X mutation or autism
22
40417392178 2002 NEUROBIOLOGY OF DISEASE 11(1):53-63
Schenck A; Van de Bor V; Bardoni B; Giangrande A
Novel features of dFMR1, the Drosophila orthologue of the fragile X mental retardation protein
33
40528392199 2003 AMERICAN JOURNAL OF HUMAN GENETICS 72(2):454-464
Nolin SL; Brown WT; Glicksman A; Houck GE; Gargano AD; Sullivan A; Biancalana V; Brondum-Nielsen K; Hjalgrim H; Holinski-Feder E; Kooy F; Longshore J; Macpherson J; Mandel JL; Matthijs G; Rousseau F; Steinbach P; Vaisanen ML; von Koskull H; Sherman SL
Expansion of the fragile X CGG repeat in females with premutation or intermediate alleles
812
40615392233 2003 AMERICAN JOURNAL ON MENTAL RETARDATION 108(3):149-160
Abbeduto L; Murphy MM; Cawthon SW; Richmond EK; Weissman MD; Karadottir S; O'Brien A
Receptive language skills of adolescents and young adults with Down or fragile X syndrome
23
40721392300 2003 NEUROSCIENCE 120(4):1005-1017
Chen L; Yun SW; Seto J; Liu W; Toth M
The fragile X mental retardation protein binds and regulates a novel class of mRNAs containing U rich target sequences
33
40820392360 2004 NATURE NEUROSCIENCE 7(2):113-117
Jin P; Zarnescu DC; Ceman S; Nakamoto M; Mowrey J; Jongens TA; Nelson DL; Moses K; Warren ST
Biochemical and genetic interaction between the fragile X mental retardation protein and the microRNA pathway
26
4091138326 1986 AMERICAN JOURNAL OF MEDICAL GENETICS 23(1-2):241-262
HAGERMAN RJ; JACKSON AW; LEVITAS A; BRADEN M; MCBOGG P; KEMPER M; MCGAVRAN L; BERRY R; MATUS I; HAGERMAN PJ
ORAL FOLIC-ACID VERSUS PLACEBO IN THE TREATMENT OF MALES WITH THE FRAGILE-X SYNDROME
1826
4101738469 1987 JOURNAL OF MEDICAL GENETICS 24(1):23-31
VEENEMA H; GERAEDTS JPM; BEVERSTOCK GC; PEARSON PL
THE FRAGILE X-SYNDROME IN A LARGE FAMILY .1. CYTOGENETIC AND CLINICAL INVESTIGATIONS
1421
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
411638674 1990 AMERICAN JOURNAL OF HUMAN GENETICS 47(2):187-195
SUTHERS GK; HYLAND VJ; CALLEN DF; OBERLE I; ROCCHI M; THOMAS NS; MORRIS CP; SCHWARTZ CE; SCHMIDT M; ROPERS HH; BAKER E; OOSTRA BA; DAHL N; WILSON PJ; HOPWOOD JJ; SUTHERLAND GR
PHYSICAL MAPPING OF NEW DNA PROBES NEAR THE FRAGILE-X MUTATION (FRAXA) BY USING A PANEL OF CELL-LINES
2664
4121638835 1991 BIOESSAYS 13(5):243-251
JORDAN BR
FRAGILE X-LINKED MENTAL-RETARDATION AND THE DIFFICULTIES OF REVERSE GENETICS
11
4131738951 1992 AMERICAN JOURNAL OF MEDICAL GENETICS 43(6):1050-1056
GLASS IA; DELMASTRO RG; LANYON WG; RAEBURN JA; KILPATRICK MW; WEBB TP; CONNOR JM
TIGHTLY LINKED POLYMORPHIC MARKERS FOR FRAGILE X-SYNDROME AND PRENATAL CYTOGENETIC DIAGNOSTIC EXPERIENCE
00
41430381151 1994 AMERICAN JOURNAL OF HUMAN GENETICS 55(2):225-237
ROUSSEAU F; HEITZ D; TARLETON J; MACPHERSON J; MALMGREN H; DAHL N; BARNICOAT A; MATHEW C; MORNET E; TEJADA I; MADDALENA A; SPIEGEL R; SCHINZEL A; MARCOS JAG; SCHORDERET DF; SCHAAP T; MACCIONI L; RUSSO S; JACOBS PA; SCHWARTZ C; MANDEL JL
A MULTICENTER STUDY ON GENOTYPE-PHENOTYPE CORRELATIONS IN THE FRAGILE-X-SYNDROME, USING DIRECT DIAGNOSIS WITH PROBE STB-12.3 - THE FIRST 2,253 CASES
119165
41515381331 1995 DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):270-279
Belser RC; Sudhalter V
Arousal difficulties in males with fragile X syndrome: A preliminary report
2024
41612381595 1997 HUMAN MOLECULAR GENETICS 6(9):1465-1472
Corbin F; Bouillon M; Fortin A; Morin S; Rousseau F; Khandjian EW
The fragile X mental retardation protein is associated with poly(A)(+) mRNA in actively translating polyribosomes
5585
41726381597 1997 HUMAN MUTATION 10(5):393-399
Wang YC; Lin ML; Lin SJ; Li YC; Li SY
Novel point mutation within intron 10 of FMR-1 gene causing fragile X syndrome
69
41812381611 1997 JOURNAL OF MEDICAL GENETICS 34(11):907-911
vanRijn MA; deVries BBA; Tibben A; vandenOuweland AMW; Halley DJJ; Niermeijer MF
DNA testing for fragile X syndrome: implications for parents and family
34
41921381767 1999 ANNALES DE GENETIQUE 42(4):197-201
Arrieta I; Criado B; Martinez B; Telez M; Nunez T; Penagarikano O; Ortega B; Lostao CM
A survey of fragile X syndrome in a sample from Spanish Basque country
34
42020382252 2003 BRAIN TOPOGRAPHY 15(3):165-171
Castren M; Paakkonen A; Tarkka IM; Ryynanen M; Partanen J
Augmentation of auditory N1 in children with fragile X syndrome
11
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
42128382317 2004 AMERICAN JOURNAL OF MEDICAL GENETICS PART A 128A(3):250-255
Penagarikano O; Gil A; Telez M; Ortega B; Flores P; Veiga I; Peixoto A; Criado B; Arrieta I
A new insight into fragile X syndrome among Basque population
00
42253784 1982 WESTERN JOURNAL OF MEDICINE 137(4):278-281
MOORE BC; GLOVER TW; KAISERMCCAW B; HECHT F
FRAGILE X-LINKED MENTAL-RETARDATION AND MACRO-ORCHIDISM
13
4231637370 1986 CHILD STUDY JOURNAL 16(4):285-296
BURD L; KERBESHIAN J
FRAGILE X-SYNDROME - DEVELOPMENTAL ASPECTS
01
424937434 1987 CLINICAL GENETICS 32(3):179-186
BORGHGRAEF M; FRYNS JP; DIELKENS A; PYCK K; VANDENBERGHE H
FRAGILE (X) SYNDROME - A STUDY OF THE PSYCHOLOGICAL PROFILE IN 23 PREPUBERTAL PATIENTS
4656
4251237493 1987 SCIENCE 237(4813):420-423
WARREN ST; ZHANG FP; LICAMELI GR; PETERS JF
THE FRAGILE-X SITE IN SOMATIC-CELL HYBRIDS - AN APPROACH FOR MOLECULAR-CLONING OF FRAGILE SITES
2971
4262037578 1988 DEVELOPMENTAL MEDICINE AND CHILD NEUROLOGY 30(2):257-261
HO HZ; GLAHN TJ; HO JC
THE FRAGILE-X SYNDROME
23
4271837672 1990 AMERICAN JOURNAL OF HUMAN GENETICS 47(2):175-180
BROWN WT
INVITED EDITORIAL - THE FRAGILE-X - PROGRESS TOWARD SOLVING THE PUZZLE
2841
4281237894 1991 PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA 88(19):8302-8306
POUSTKA A; DIETRICH A; LANGENSTEIN G; TONIOLO D; WARREN ST; LEHRACH H
PHYSICAL MAP OF HUMAN XQ27-QTER - LOCALIZING THE REGION OF THE FRAGILE-X MUTATION
775
4291837897 1991 SCIENCE 252(5009):1097-1102
OBERLE I; ROUSSEAU F; HEITZ D; KRETZ C; DEVYS D; HANAUER A; BOUE J; BERTHEAS MF; MANDEL JL
INSTABILITY OF A 550 BASE PAIR DNA SEGMENT AND ABNORMAL METHYLATION IN FRAGILE X-SYNDROME
394835
4302537959 1992 ANNALS OF MEDICINE 24(6):453-456
POUSTKA A
FRAGILE-X SYNDROME - MOLECULAR ANALYSIS REVEALS A NEW MECHANISM OF MUTATION IN HUMAN GENETIC-DISEASES
00
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
43118371081 1993 CLINICAL GENETICS 44(3):129-138
BUTLER MG; PRATESI R; WATSON MS; BREG WR; SINGH DN
ANTHROPOMETRIC AND CRANIOFACIAL PATTERNS IN MENTALLY-RETARDED MALES WITH EMPHASIS ON THE FRAGILE-X SYNDROME
48
43214371110 1993 JOURNAL OF DEVELOPMENTAL AND BEHAVIORAL PEDIATRICS 14(5):328-335
MAZZOCCO MMM; PENNINGTON BF; HAGERMAN RJ
THE NEUROCOGNITIVE PHENOTYPE OF FEMALE CARRIERS OF FRAGILE-X - ADDITIONAL EVIDENCE FOR SPECIFICITY
6887
43320371143 1993 PEDIATRICS 91(2):321-329
FREUND LS; REISS AL; ABRAMS MT
PSYCHIATRIC-DISORDERS ASSOCIATED WITH FRAGILE-X IN THE YOUNG FEMALE
5476
43427371183 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):474-481
HAGERMAN RJ; WILSON P; STALEY LW; LANG KA; FAN T; UHLHORN C; JEWELLSMART S; HULL C; DRISKO J; FLOM K; TAYLOR AK
EVALUATION OF SCHOOL-CHILDREN AT HIGH-RISK FOR FRAGILE-X-SYNDROME UTILIZING BUCCAL CELL FMR-1 TESTING
1736
43511371243 1994 JOURNAL OF THE AMERICAN ACADEMY OF CHILD AND ADOLESCENT PSYCHIATRY 33(2):256-264
DORN MB; MAZZOCCO MMM; HAGERMAN RJ
BEHAVIORAL AND PSYCHIATRIC-DISORDERS IN ADULT MALE CARRIERS OF FRAGILE-X
2131
43620371259 1995 AMERICAN JOURNAL OF HUMAN GENETICS 56(5):1042-1051
QUAN F; ZONANA J; GUNTER K; PETERSON KL; MAGENIS RE; POPOVICH BW
AN ATYPICAL CASE OF FRAGILE-X SYNDROME CAUSED BY A DELETION THAT INCLUDES THE FMRI GENE
1629
43719371332 1995 DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):280-292
Sobesky WE; Porter D; Pennington BF; Hagerman RJ
Dimensions of shyness in fragile X females
1217
43822371364 1995 JOURNAL OF CLINICAL AND EXPERIMENTAL NEUROPSYCHOLOGY 17(4):518-528
HINTON VJ; HALPERIN JM; DOBKIN CS; DING XH; BROWN WT; MIEZEJESKI CM
COGNITIVE AND MOLECULAR ASPECTS OF FRAGILE-X
57
43915371397 1996 AMERICAN JOURNAL OF HUMAN GENETICS 59(3):540-546
Vaisanen ML; Haataja R; Leisti L
Decrease in the CGG(n) trinucleotide repeat mutation of the fragile X syndrome to normal size range during paternal transmission
49
44013371419 1996 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):246-251
Godfraind JM; Reyniers E; DeBoulle K; DHooge R; DeDeyn PP; Bakker CE; Oostra BA; Kooy RF; Willems PJ
Long-term potentiation in the hippocampus of fragile X knockout mice
2231
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
44119371455 1996 ARCHIVES DE PEDIATRIE 3(8):814-821
Mornet E; SimonBouy B
Molecular biology of fragile X syndrome: Applications to genetic counselling and molecular diagnosis
34
4425371488 1996 JOURNAL OF BIOLOGICAL CHEMISTRY 271(38):22937-22940
Wang YH; Griffith J
Methylation of expanded CCG triplet repeat DNA from fragile X syndrome patients enhances nucleosome exclusion
122
44310371675 1998 JOURNAL OF BIOLOGICAL CHEMISTRY 273(25):15521-15527
Brown V; Small K; Lakkis L; Feng Y; Gunter C; Wilkinson KD; Warren ST
Purified recombinant Fmrp exhibits selective RNA binding as an intrinsic property of the fragile X mental retardation protein
3662
44418371744 1999 AMERICAN JOURNAL OF MEDICAL GENETICS 84(3):184-190
Patsalis PC; Sismani C; Hettinger JA; Boumba I; Georgiou I; Stylianidou G; Anastasiadou V; Koukoulli R; Pagoulatos G; Syrrou M
Molecular screening of fragile X (FRAXA) and FRAXE mental retardation syndromes in the Hellenic population of Greece and Cyprus: Incidence, genetic variation, and stability
718
44520371753 1999 AMERICAN JOURNAL OF MEDICAL GENETICS 84(3):245-249
Reyniers E; Martin JJ; Cras P; Van Marck E; Handig I; Jorens HZJ; Oostra BA; Kooy RF; Willems PJ
Postmortem examination of two fragile X brothers with an FMR1 full mutation
1419
44614371866 2000 AMERICAN JOURNAL ON MENTAL RETARDATION 105(4):286-299
Kau ASM; Reider EE; Payne L; Meyer WA; Freund L
Early behavior signs of psychiatric phenotypes in fragile X syndrome
24
44720371867 2000 ANNALES DE GENETIQUE 43(1):29-34
Gonzalez-del Angel A; Vidal S; Saldana Y; del Castillo V; Alcantara MA; Macias M; Luna JP; Orozco L
Molecular diagnosis of the fragile X and FRAXE syndromes in patients with mental retardation of unknown cause in Mexico
23
44820371949 2000 MOLECULAR BRAIN RESEARCH 80(1):17-25
Todd PK; Mack KJ
Sensory stimulation increases cortical expression of the fragile X mental retardation protein in vivo
1517
44917371992 2001 AMERICAN JOURNAL ON MENTAL RETARDATION 106(1):16-27
Bailey DB; Hatton DD; Tassone F; Skinner M; Taylor AK
Variability in FMRP and early development in males with fragile X syndrome
1312
45018372007 2001 CELL 107(5):591-603
Zhang YQ; Bailey AM; Matthies HJG; Renden RB; Smith MA; Speese SD; Rubin GM; Broadie K
Drosophila fragile X-related gene regulates the MAP1B homolog Futsch to control synaptic structure and function
3671
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
45110372093 2002 AMERICAN JOURNAL OF HUMAN GENETICS 71(4):923-932
Coffee B; Zhang FP; Ceman S; Warren ST; Reines D
Histone modifications depict an aberrantly heterochromatinized FMR1 gene in fragile X syndrome
27
4525372114 2002 CURRENT BIOLOGY 12(15):1331-1335
Inoue SB; Shimoda M; Nishinokubi I; Siomi MC; Okamura M; Nakamura A; Kobayashi S; Ishida N; Siomi H
A role for the Drosophila fragile X-related gene in circadian output
913
45311372340 2004 JOURNAL OF NEUROSCIENCE 24(11):2648-2655
Antar LN; Afroz R; Dictenberg JB; Carroll RC; Bassell GJ
Metabotropic glutamate receptor activation regulates Fragile X mental retardation protein and Fmr1 mRNA localization differentially in dendrites and at synapses
00
454036110 1983 AMERICAN JOURNAL OF MENTAL DEFICIENCY 87(4):372-376
PUESCHEL SM; HAYS RM; MENDOZA T
FAMILIAL X-LINKED MENTAL-RETARDATION SYNDROME ASSOCIATED WITH MINOR CONGENITAL-ANOMALIES, MACRO-ORCHIDISM, AND FRAGILE X-CHROMOSOME
68
455636188 1984 AMERICAN JOURNAL OF MEDICINE 77(4):602-611
BRANDA RF; ARTHUR DC; WOODS WG; DANZL TJ; KING RA
FOLATE METABOLISM AND CHROMOSOMAL STABILITY IN THE FRAGILE-X SYNDROME
514
4561136399 1986 JOURNAL OF THE AMERICAN ACADEMY OF CHILD AND ADOLESCENT PSYCHIATRY 25(5):641-644
WRIGHT HH; YOUNG SR; EDWARDS JG; ABRAMSON RK; DUNCAN J
FRAGILE X-SYNDROME IN A POPULATION OF AUTISTIC-CHILDREN
1621
457536411 1987 AMERICAN JOURNAL OF DISEASES OF CHILDREN 141(2):184-187
HAGERMAN RJ; ALTSHULSTARK D; MCBOGG P
RECURRENT OTITIS-MEDIA IN THE FRAGILE X-SYNDROME
914
4581736423 1987 ANNALS OF HUMAN GENETICS 51:107-124
GIANNELLI F; MORRIS AH; GARRETT C; DAKER M; THURSTON C; SMITH CAB
GENETIC-HETEROGENEITY OF X-LINKED MENTAL-RETARDATION WITH FRAGILE-X - ASSOCIATION OF TIGHT LINKAGE TO FACTOR-IX AND INCOMPLETE PENETRANCE IN MALES
716
459336484 1987 NEUROPSYCHOLOGIA 25(6):881-891
GRIGSBY JP; KEMPER MB; HAGERMAN RJ
DEVELOPMENTAL GERSTMANN SYNDROME WITHOUT APHASIA IN FRAGILE-X SYNDROME
1627
4601036521 1988 AMERICAN JOURNAL OF MEDICAL GENETICS 30(1-2):213-225
WOLFF PH; GARDNER J; LAPPEN J; PACCIA J; MERYASH D
VARIABLE EXPRESSION OF THE FRAGILE-X SYNDROME IN HETEROZYGOUS FEMALES OF NORMAL INTELLIGENCE
2835
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
4611836707 1990 JOURNAL OF BONE AND JOINT SURGERY-AMERICAN VOLUME 72A(6):889-896
DAVIDS JR; HAGERMAN RJ; EILERT RE
ORTHOPEDIC ASPECTS OF FRAGILE-X SYNDROME
013
4622036982 1992 HUMAN GENETICS 90(1-2):55-61
ERSTER SH; BROWN WT; GOONEWARDENA P; DOBKIN CS; JENKINS EC; PERGOLIZZI RG
POLYMERASE CHAIN-REACTION ANALYSIS OF FRAGILE X-MUTATIONS
1830
46329361024 1993 AMERICAN JOURNAL OF DISEASES OF CHILDREN 147(11):1236-1241
HULL C; HAGERMAN RJ
A STUDY OF THE PHYSICAL, BEHAVIORAL, AND MEDICAL PHENOTYPE, INCLUDING ANTHROPOMETRIC MEASURES, OF FEMALES WITH FRAGILE-X SYNDROME
2738
46419361138 1993 NATURE GENETICS 4(4):335-340
DEVYS D; LUTZ Y; ROUYER N; BELLOCQ JP; MANDEL JL
THE FMR-1 PROTEIN IS CYTOPLASMIC, MOST ABUNDANT IN NEURONS AND APPEARS NORMAL IN CARRIERS OF A FRAGILE X PREMUTATION
169277
46514361163 1994 AMERICAN JOURNAL OF MEDICAL GENETICS 51(4):358-363
HAY DA
DOES IQ DECLINE WITH AGE IN FRAGILE-X A METHODOLOGICAL CRITIQUE
1213
46627361328 1995 DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):230-241
Brun C; Obiols JE; Cheema A; OConnor R; Riddle J; DiMaria M; WrightTalamante C; Hagerman R
Longitudinal IQ changes in fragile X females
11
46716361347 1995 EMBO JOURNAL 14(21):5358-5366
ZHANG Y; OCONNOR JP; SIOMI MC; SRINIVASAN S; DUTRA A; NUSSBAUM RL; DREYFUSS G
THE FRAGILE-X MENTAL-RETARDATION SYNDROME PROTEIN INTERACTS WITH NOVEL HOMOLOGS FXR1 AND FXR2
63111
46818361667 1998 HUMAN REPRODUCTION 13(5):1184-1187
Conway GS; Payne NN; Webb J; Murray A; Jacobs PA
Fragile X premutation screening in women with premature ovarian failure
831
46912361674 1998 JOURNAL OF AUTISM AND DEVELOPMENTAL DISORDERS 28(6):509-517
Mazzocco MMM; Baumgardner T; Freund LS; Reiss AL
Social functioning among girls with fragile X or Turner syndrome and their sisters
811
47020361690 1998 JOURNAL OF PEDIATRICS 133(3):363-365
Meyer GA; Blum NJ; Hitchcock W; Fortina P
Absence of the fragile X CGG trinucleotide repeat expansion in girls diagnosed with a pervasive developmental disorder
03
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
47117361695 1998 NEUROPSYCHOLOGIA 36(11):1239-1246
Cornish KM; Munir F; Cross G
The nature of the spatial deficit in young females with Fragile-X syndrome: A neuropsychological and molecular perspective
1014
4724361756 1999 AMERICAN JOURNAL OF MEDICAL GENETICS 84(3):272-276
Currie JR; Brown WT
KH domain-containing proteins of yeast: Absence of a fragile X gene homologue
04
47317361771 1999 BIOCHEMICAL JOURNAL 343:517-523
Tamanini F; van Unen L; Bakker C; Sacchi N; Galjaard H; Oostra BA; Hoogeveen AT
Oligomerization properties of fragile-X mental-retardation protein (FMRP) and the fragile-X-related proteins FXR1P and FXR2P
1520
47421361934 2000 JOURNAL OF MEDICAL GENETICS 37(1):77-79
Beresford RG; Tatlidil C; Riddell DC; Welch JP; Ludman MD; Neumann PE; Greer WL
Absence of fragile X syndrome in Nova Scotia
44
47518362051 2001 NUCLEIC ACIDS RESEARCH 29(11):2276-2283
Li ZZ; Zhang YY; Ku L; Wilkinson KD; Warren ST; Feng Y
The fragile X mental retardation protein inhibits translation via interacting with mRNA
4667
47610362055 2001 PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA 98(13):7101-7106
Greenough WT; Klintsova AY; Irwin SA; Galvez R; Bates KE; Weiler IJ
Synaptic regulation of protein synthesis and the fragile X protein
3049
47718362056 2001 PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA 98(15):8844-8849
Schenck A; Bardoni B; Moro A; Bagni C; Mandel JL
A highly conserved protein family interacting with the fragile X mental retardation protein (FMRP) and displaying selective interactions with FMRP-related proteins FXR1P and FXR2P
2038
4783362100 2002 AMERICAN JOURNAL OF MEDICAL GENETICS 111(4):381-387
Steinhausen HC; von Gontard A; Spohr HL; Hauffa BP; Eiholzer U; Backes M; Willms J; Malin Z
Behavioral phenotypes in four mental retardation syndromes: Fetal alcohol syndrome, Prader-Willi syndrome, fragile X syndrome, and tuberosis sclerosis
00
47916362187 2002 NUCLEIC ACIDS RESEARCH 30(14):3278-3285
Pietrobono R; Pomponi MG; Tabolacci E; Oostra B; Chiurazzi P; Neri G
Quantitative analysis of DNA demethylation and transcriptional reactivation of the FMR1 gene in fragile X cells treated with 5-azadeoxycytidine
36
48018362200 2003 AMERICAN JOURNAL OF HUMAN GENETICS 72(4):869-878
Jacquemont S; Hagerman RJ; Leehey M; Grigsby J; Zhang L; Brunberg JA; Greco C; Des Portes V; Jardini T; Levine R; Berry-Kravis E; Brown WT; Schaeffer S; Kissel J; Tassone F; Hagerman PJ
Fragile X premutation tremor/ataxia syndrome: Molecular, clinical, and neuroimaging correlates
1019
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
48125362251 2003 BRAIN RESEARCH 972(1-2):9-15
Segal M; Kreher U; Greenberger V; Braun K
Is fragile X mental retardation protein involved in activity-induced plasticity of dendritic spines?
01
4828362303 2003 PEDIATRICS 111(2):407-416
Bailey DB; Skinner D; Sparkman KL
Discovering fragile X syndrome: Family experiences and perceptions
44
4836362336 2004 JOURNAL OF DEVELOPMENTAL AND BEHAVIORAL PEDIATRICS 25(1):21-27
Mirrett PL; Bailey DB; Roberts JE; Hatton DD
Developmental screening and detection of developmental delays in infants and toddlers with fragile X syndrome
00
48423536 1982 AMERICAN JOURNAL OF DISEASES OF CHILDREN 136(5):392-398
CARPENTER NJ; LEICHTMAN LG; SAY B
FRAGILE X-LINKED MENTAL-RETARDATION - A SURVEY OF 65 PATIENTS WITH MENTAL-RETARDATION OF UNKNOWN ORIGIN
4865
485335233 1984 PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES 81(24):7855-7859
SZABO P; PURRELLO M; ROCCHI M; ARCHIDIACONO N; ALHADEFF B; FILIPPI G; TONIOLO D; MARTINI G; LUZZATTO L; SINISCALCO M
CYTOLOGICAL MAPPING OF THE HUMAN GLUCOSE-6-PHOSPHATE-DEHYDROGENASE GENE DISTAL TO THE FRAGILE-X SITE SUGGESTS A HIGH-RATE OF MEIOTIC RECOMBINATION ACROSS THIS SITE
1771
4861935675 1990 AMERICAN JOURNAL OF HUMAN GENETICS 47(3):395-402
SOOD R; MULLIGAN LM; POON R; WHITE BN; HOLDEN JJA
GENETIC-MAPPING OF 2 NEW DNA MARKERS IN XQ26-Q28 RELATIVE TO THE FRAGILE-X SYNDROME LOCUS
37
4871835858 1991 GENOMICS 10(3):576-582
SUTHERS GK; MULLEY JC; VOELCKEL MA; DAHL N; VAISANEN ML; STEINBACH P; GLASS IA; SCHWARTZ CE; VANOOST BA; THIBODEAU SN; HAITES NE; OOSTRA BA; SCHINZEL A; CARBALLO M; MORRIS CP; HOPWOOD JJ; SUTHERLAND GR
LINKAGE HOMOGENEITY NEAR THE FRAGILE-X LOCUS IN NORMAL AND FRAGILE-X FAMILIES
913
48817351057 1993 AMERICAN JOURNAL OF HUMAN GENETICS 53(5):1064-1073
LOESCH DZ; HUGGINS R; HAY DA; GEDEON AK; MULLEY JC; SUTHERLAND GR
GENOTYPE-PHENOTYPE RELATIONSHIPS IN FRAGILE-X SYNDROME - A FAMILY STUDY
4360
4898351336 1995 DEVELOPMENTAL BRAIN DYSFUNCTION 8(4-6):336-344
Hagerman RJ; Riddle JE; Roberts LS; Breese K; Fulton M
Survey of the efficacy of clonidine in fragile X syndrome
1010
49013351375 1995 JOURNAL OF MEDICAL GENETICS 32(12):925-929
KIRCHGESSNER CU; WARREN ST; WILLARD HF
X INACTIVATION OF THE FMR1 FRAGILE-X MENTAL-RETARDATION GENE
512
#LCRNCRNodes / Date / Journal / AuthorsLCSGCS
49123351389 1995 PRENATAL DIAGNOSIS 15(9):801-807
CASTELLVIBEL S; MILA M; SOLER A; CARRIO A; SANCHEZ A; VILLA M; JIMENEZ MD; ESTIVILL X
PRENATAL-DIAGNOSIS OF FRAGILE-X SYNDROME - (CGG)(N) EXPANSION AND METHYLATION OF CHORIONIC VILLUS SAMPLES
26
49221351425 1996 AMERICAN JOURNAL OF MEDICAL GENETICS 64(2):287-292
Brown WT; Houck GE; Ding XH; Zhong N; Nolin S; Glicksman A; Dobkin C; Jenkins EC
Reverse mutations in the fragile X syndrome
918
49317351515 1996 SOMATIC CELL AND MOLECULAR GENETICS 22(6):435-441
Eberhart DE; Warren ST
Nuclease sensitivity of permeabilized cells confirms altered chromatin formation at the fragile X locus
614
49422351527 1997 AMERICAN JOURNAL OF HUMAN GENETICS 61(3):660-667
deVries BBA; vandenOuweland AMW; Mohkamsing S; Duivenvoorden HJ; Mol E; Gelsema K; vanRijn M; Halley DJJ; Sandkuijl LA; Oostra BA; Tibben A; Niermeijer MF
Screening and diagnosis for the fragile X syndrome among the mentally retarded: An epidemiological and psychological survey
3570
49525351571 1997 BRAZILIAN JOURNAL OF GENETICS 20(4):731-739
Mingroni-Netto RC; Pavanello RCM; Otto PA; Vianna-Morgante AM
Experience with molecular and cytogenetic diagnosis of fragile X syndrome in Brazilian families
22
49621351594 1997 HUMAN MOLECULAR GENETICS 6(7):971-979
Moutou C; Vincent MC; Biancalana V; Mandel JL
Transition from premutation to full mutation in fragile X syndrome is likely to be prezygotic
1833
4977351615 1997 JOURNAL OF THEORETICAL BIOLOGY 188(1):53-67
Bat O; Kimmel M; Axelrod DE
Computer simulation of expansions of DNA triplet repeats in the fragile X syndrome and Huntington's disease
14
4986351724 1999 AMERICAN JOURNAL OF MEDICAL GENETICS 83(4):248-252
Weiler IJ; Greenough WT
Synaptic synthesis of the Fragile X protein: Possible involvement in synapse maturation and elimination
2742
49919351732 1999 AMERICAN JOURNAL OF MEDICAL GENETICS 83(4):302-307
Parvari R; Mumm S; Galil A; Manor E; Bar-David Y; Carmi R
Deletion of 8.5 Mb, including the FMR1 gene, in a male with the fragile X syndrome phenotype and overgrowth
26
50026351854 2000 AMERICAN JOURNAL OF MEDICAL GENETICS 94(3):232-236
Tassone F; Hagerman RJ; Loesch DZ; Lachiewicz A; Taylor AK; Hagerman PJ
Fragile X males with unmethylated, full mutation trinucleotide repeat expansions have elevated levels of FMR1 messenger RNA
1623

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